在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. RARS2 Antibody, HRP conjugated

RARS2 Antibody, HRP conjugated

  • 中文名稱：
    RARS2兔多克隆抗體, HRP偶聯(lián)
  • 貨號：
    CSB-PA732918LB01HU
  • 規(guī)格：
    ￥880
  • 其他：

產(chǎn)品詳情

  • 產(chǎn)品名稱：
    Rabbit anti-Homo sapiens (Human) RARS2 Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    RARS2
  • 別名：
    Probable arginine--tRNA ligase, mitochondrial (EC 6.1.1.19) (Arginyl-tRNA synthetase) (ArgRS), RARS2, RARSL
  • 宿主：
    Rabbit
  • 反應(yīng)種屬：
    Human
  • 免疫原：
    Recombinant Human Probable arginine--tRNA ligase, mitochondrial protein (230-578aa)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    HRP
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式：
    Liquid
  • 應(yīng)用范圍：
    ELISA
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評價

靶點詳情

  • 基因功能參考文獻：
    1. Characteristic neuroradiological abnormalities of PCH6 such as vermis and cerebellar hypoplasia and progressive pontocerebellar atrophy may be missing in patients with RARS2 mutations PMID: 27769281
    2. RARS2 gene mutations can cause a metabolic neurodegenerative disease manifesting primarily as early onset epileptic encephalopathies with post-natal microcephaly, without pontocerebellar hypoplasia. PMID: 26970947
    3. Mutations in the RARS2 promoter are likely to represent a new causal mechanism of pontocerebellar hypoplasia. PMID: 25809939
    4. Molecular investigations of RARS2 disclosed the c.25A>G/p.I9V and the c.1586+3A>T in family A. PMID: 22569581
    5. mutations in the gene encoding mitochondrial arginyl-tRNA synthetase, RARS2, may have a role in pontocerebellar hypoplasia type 6 [case report] PMID: 22086604

    顯示更多

    收起更多

  • 相關(guān)疾病：
    Pontocerebellar hypoplasia 6 (PCH6)
  • 亞細胞定位：
    Mitochondrion matrix.
  • 蛋白家族：
    Class-I aminoacyl-tRNA synthetase family
  • 數(shù)據(jù)庫鏈接：

    HGNC: 21406

    OMIM: 611523

    KEGG: hsa:57038

    STRING: 9606.ENSP00000358549

    UniGene: Hs.485910



主站蜘蛛池模板： 蜜臀av综合网| 久9re热视频这里只有精品| 风流老熟女一区二区三区| 亚洲午夜无码毛片av久久京东热| 怡春院久久国语视频免费| 岛国在线无码高清视频| 99久久国产综合精品成人影院| 国产精品人人爽人人做我的可爱| 免费女人高潮流视频在线| 久久精品道一区二区三区| 欧美一区二区三区红桃小说| 少妇无码一区二区三区| 日韩精品人妻系列一区二区三区| 日本一丰满一bbw| 中国极品少妇videossexhd| 麻豆国产97在线 | 欧美| 亚洲一区波多野结衣在线| 无码专区6080yy国产电影| 久久久久九九精品影院| 欧美性猛交xxxx富婆| 欧洲精品一卡2卡三卡4卡影视| 鲁鲁狠狠狠7777一区二区| 一出一进一爽一粗一大视频| 国产成人啪精品视频免费网站软件| 天天躁夜夜躁狠狠综合 | 日韩人妻无码一区二区三区久久99| 中国人妻被两个老外三p | 亚洲成av人片在www色猫咪| 9l国产精品久久久久尤物| 亚洲 丝袜 制服 欧美 另类| 久久久肥妇熟女ⅹxxx毛片| 欧美人与动牲猛交a欧美精品 | 40岁成熟女人牲交片20分钟| 亚洲人成影院在线无码按摩店| 2018高清日本一道国产-在| 久久久无码精品亚洲日韩按摩| 亚洲伊人色欲综合网| 久久亚洲道色宗和久久| 国产精品女视频一区二区| 风韵丰满熟妇啪啪区老老熟妇| 免费香蕉成视频人网站|