在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

HOGA1 Antibody, FITC conjugated

  • 中文名稱(chēng):
    HOGA1兔多克隆抗體, FITC偶聯(lián)
  • 貨號(hào):
    CSB-PA771464LC01HU
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱(chēng):
    Rabbit anti-Homo sapiens (Human) HOGA1 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    HOGA1
  • 別名:
    HOGA1 antibody; C10orf65 antibody; DHDPSL antibody; 4-hydroxy-2-oxoglutarate aldolase antibody; mitochondrial antibody; EC 4.1.3.16 antibody; Dihydrodipicolinate synthase-like antibody; DHDPS-like protein antibody; Probable 2-keto-4-hydroxyglutarate aldolase antibody; Probable KHG-aldolase antibody; Protein 569272 antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human
  • 免疫原:
    Recombinant Human 4-hydroxy-2-oxoglutarate aldolase, mitochondrial protein (1-164AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標(biāo)記方式:
    FITC
  • 克隆類(lèi)型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能:
    Catalyzes the final step in the metabolic pathway of hydroxyproline.
  • 基因功能參考文獻(xiàn):
    1. Results show that HOGA1 harboring mutations found in primary hyperoxaluria is thermally unstable and targeted for proteolytic degradation leading to an absolute loss of function. PMID: 27096395
    2. Among the seven patients identified with HOGA1 mutations the median onset of clinical symptoms was 1.8 years. Five patients initially presented with urolithiasis, and two other patients presented with urinary tract infection. PMID: 25972204
    3. Our results strongly suggest HOGA1 as a major cause of PH, indicate a greater genetic heterogeneity of hyperoxaluria, and point to a favorable outcome of type III in the context of PH despite incomplete or absent biochemical remission PMID: 22781098
    4. seven different mutations were identified in primary hyperoxaluria type 3 PMID: 22391140
    5. Two crystal forms of DHDPSL were obtained, both of which diffracted X-rays to approximately 2.0 A resolution PMID: 22232173
    6. hHOGA utilizes a type I aldolase reaction mechanism, but employs novel residue interactions for substrate binding PMID: 21998747
    7. Detection of HOGA1 variants in idiopathic calcium oxalate urolithiasis also suggests HOGA1 may be a predisposing factor for this condition PMID: 21896830
    8. DHDPSL is the gene encoding 4-hydroxy-2-oxoglutarate aldolase, catalyzing the final step in the metabolic pathway of hydroxyproline. PMID: 20797690

    顯示更多

    收起更多

  • 相關(guān)疾病:
    Hyperoxaluria primary 3 (HP3)
  • 亞細(xì)胞定位:
    Mitochondrion.
  • 蛋白家族:
    DapA family
  • 數(shù)據(jù)庫(kù)鏈接:

    HGNC: 25155

    OMIM: 613597

    KEGG: hsa:112817

    STRING: 9606.ENSP00000359680

    UniGene: Hs.180346



主站蜘蛛池模板: 人妻无码中字在线a| 亚洲一区二区三区av无码| 亚洲欧洲av综合色无码| 精品无码欧美黑人又粗又| 四虎影视无码永久免费| 国产成+人+综合+亚洲欧美| 亚洲精品久久夜色撩人男男小说| 国产特黄级aaaaa片免| 国产精品久久久久野外| 久久亚洲精品无码播放| 久久久www成人免费看片| 巨爆乳中文字幕巨爆区巨爆乳无码| 麻豆成人精品国产免费| 国产成人三级一区二区在线观看一| 国产农村乱对白刺激视频| 天天拍夜夜添久久精品| 亚洲国产成人精品无码区二本| 夜夜爽妓女8888888视频| 天天天天躁天天爱天天碰2018| 日本老妇人乱xxy| 亚洲 欧美 日产 综合 在线| 夜夜揉揉日日人人| 亚洲乱码国产一区三区| 精品国产不卡一区二区三区| 亚洲性无码av在线| 97久久超碰国产精品旧版麻豆| 国产人妻精品午夜福利免费| av色综合久久天堂av色综合在| 玖玖资源站最稳定网址| 欧美xxxxx在线观看| 人妻精品动漫h无码中字| 少妇人妻偷人精品视蜜桃| 国产成人无码av在线影院| 亚洲制服丝中文字幕| 久久狠狠色噜噜狠狠狠狠97| www国产成人免费观看视频| 精品成人免费国产片| 人人超人人超碰超国产| 亚洲一区二区三区丝袜| 亚洲日产av中文字幕无码偷拍| 青青草99久久精品国产综合|