在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

GLRX5 Antibody, FITC conjugated

  • 中文名稱:
    GLRX5兔多克隆抗體, FITC偶聯(lián)
  • 貨號(hào):
    CSB-PA769767LC01HU
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) GLRX5 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    GLRX5
  • 別名:
    C14orf87 antibody; Chromosome 14 open reading frame 87 antibody; FLB4739 antibody; GLRX 5 antibody; Glrx5 antibody; GLRX5_HUMAN antibody; Glutaredoxin 5 homolog antibody; Glutaredoxin related protein 5 antibody; Glutaredoxin-related protein 5 antibody; Glutaredoxin5 antibody; GRX5 antibody; MGC14129 antibody; mitochondrial antibody; Monothiol glutaredoxin-5 antibody; PRO1238 antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human
  • 免疫原:
    Recombinant Human Glutaredoxin-related protein 5, mitochondrial protein (32-157AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標(biāo)記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能:
    Monothiol glutaredoxin involved in mitochondrial iron-sulfur (Fe/S) cluster transfer. Receives 2Fe/2S clusters from scaffold protein ISCU and mediates their transfer to apoproteins, to the 4Fe/FS cluster biosynthesis machinery, or export from mitochondrion. Required for normal regulation of hemoglobin synthesis by the iron-sulfur protein ACO1.
  • 基因功能參考文獻(xiàn):
    1. GLRX5 rs1007814 showed a statistically marginally significant difference between cases and controls in genotype frequency (case/control: CC 1:6; CT 112:78; TT 752:505, P=0.049361), but no significant differences in allele distribution [odds ratio (OR)=0.852805]In men, we found a minor difference in the genotype frequency (case/control: CC 0:3; CT 72:36; TT 411:280, P=0.037370) and not in allele distribution (OR=1.142857) PMID: 27893590
    2. Patients with GLRX5-associated variant nonketotic hyperglycemia had normal development with childhood-onset spastic paraplegia, spinal lesion, and optic atrophy. PMID: 24334290
    3. crystal structure of GLRX5 revealed a tetrameric organization with the [2Fe-2S] clusters buried in the interior and shielded from the solvent by the conserved beta1-alpha2 loop PMID: 21029046
    4. Glutaredoxin 5 deficiency causes sideroblastic anemia by specifically impairing heme biosynthesis and depleting cytosolic iron in human erythroblasts PMID: 20364084
    5. No GLRX5 mutations were found among sixty CSA probands examined PMID: 19731322
    6. Mutations in GLRX5 is associated with sideroblastic-like microcytic anemia and iron overload PMID: 17485548

    顯示更多

    收起更多

  • 相關(guān)疾病:
    Anemia, sideroblastic, 3, pyridoxine-refractory (SIDBA3); Spasticity, childhood-onset, with hyperglycinemia (SPAHGC)
  • 亞細(xì)胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Glutaredoxin family, Monothiol subfamily
  • 數(shù)據(jù)庫(kù)鏈接:

    HGNC: 20134

    OMIM: 609588

    KEGG: hsa:51218

    STRING: 9606.ENSP00000328570

    UniGene: Hs.744943



主站蜘蛛池模板: 欧美大屁股xxxxhd黑色| 国产人妻高清国产拍精品| 国产精品美脚玉足脚交欧美| 99热门精品一区二区三区无码 | 动漫精品啪啪一区二区三区| 精品人妻无码一区二区三区抖音| 国产人成网线在线播放va| 免费无遮挡很爽很污很黄的网站| av无码中出一区二区三区| 日本二区三区欧美亚洲国产| 无码办公室丝袜ol中文字幕| 亚洲欧美精品aaaaaa片| 337人体做爰大胆视频| 国产福利姬喷水福利在线观看| 18禁精品久久久国产精品久久久| 夜夜夜夜猛噜噜噜噜噜| 男女一边摸一边做爽爽| 色狠狠色噜噜av天堂一区| 国产精品成人免费一区久久羞羞| 国产午夜手机精彩视频| 欧美牲交a欧牲交aⅴ久久| 吃奶呻吟打开双腿做受在线视频| 曰本大码熟中文字幕| 狂野欧美激情性xxxx按摩| 扒开双腿疯狂进出爽爽爽视频| 五月婷婷俺也去开心| 在线 无码 中文字幕 强 乱| 亚洲性色av性色在线观看| 亚洲国产成人一区二区三区| 性色欲网站人妻丰满中文久久不卡| 欧美 国产 综合 欧美 视频| 国产成人无码av在线影院| 国产交换配乱婬视频偷网站| 2020无码天天喷水天天爽| 久久亚洲精品11p| 99尹人香蕉国产免费天天| 国产成+人+综合+亚洲欧美 | 午夜成人亚洲理论片在线观看| 久久丫精品系列| 精品无码国产av一区二区| 亚洲色大成网站www永久一区|