在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

AGA Antibody

  • 中文名稱:
    AGA兔多克隆抗體
  • 貨號:
    CSB-PA001423LA01HU
  • 規格:
    ¥440
  • 圖片:
    • Western blot
      All lanes: AGA antibody at 10µg/ml
      Lane 1: 293T whole cell lysate
      Lane 2: Mouse muscle tissue
      Secondary
      Goat polyclonal to rabbit IgG at 1/10000 dilution
      Predicted band size: 38 kDa
      Observed band size: 38 kDa
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) AGA Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    AGA
  • 別名:
    Aga antibody; AGU antibody; Aspartylglucosaminidase antibody; Aspartylglucosylamine deaspartylase antibody; Aspartylglycosaminuria antibody; ASPG_HUMAN antibody; ASRG antibody; GA antibody; Glycosylasparaginase antibody; Glycosylasparaginase beta chain antibody; N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase antibody; N4 (N acetyl beta glucosaminyl) L asparagine amidase antibody; N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human, Mouse
  • 免疫原:
    Recombinant Human N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase protein (206-346AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,AGA Antibody (CSB-PA001423LA01HU),的標記方式是Non-conjugated。對于AGA Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA001423LB01HU AGA Antibody, HRP conjugated ELISA
    FITC CSB-PA001423LC01HU AGA Antibody, FITC conjugated
    Biotin CSB-PA001423LD01HU AGA Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA, WB
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:1000-1:5000
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Cleaves the GlcNAc-Asn bond which joins oligosaccharides to the peptide of asparagine-linked glycoproteins.
  • 基因功能參考文獻:
    1. 1.8A resolution crystal structure of mature G172D mutant of a model missense GA corresponding to a Canadian aspartylglucosaminuria allele; studied the effect of its single amino acid change on substrate processing PMID: 28457719
    2. We show that gene-silenced cells show specifically reduced AGA activity and store globotriaosylceramide. In gene-silenced cells, release of the neurotransmitter acetylcholine is significantly reduced, demonstrating that this model may be used to study specific neuronal functions such as neurotransmitter release in Fabry disease PMID: 27471012
    3. study reports 2 novel aspartylglucosaminidase gene mutations, one in Qatari twins with an early, perinatal presentation not previously described for aspartylglucosaminuria and the other in 3 Turkish children with newly diagnosed aspartylglucosaminuria and a more classical disease course PMID: 23271757
    4. [review] Natural killer (NK) cell tumors, subtypes of myeloid leukemias and T-cell lymphomas respond to ASNase; ovarian carcinomas and other solid tumors have been proposed as additional targets for ASNase, with a potential role for glutaminase. activity. PMID: 21854356
    5. Molecular mechanism for the autoproteolytic activation of aspartylglucosaminidase. PMID: 14616088
    6. A new point mutation, c.44T>G, found in a Finnish compound heterozygote causes a L15R AA substitution in the signal sequence of the AGA enzyme, affecting AGA translocation by altering a critical hydrophobic core structure in the signal sequence. PMID: 15365992
    7. aspartylglucosaminidase may have a role in development of congenital disorders of glycosylation type I PMID: 16435229
    8. The amino acid substitutions in aspartylglucosaminidase responsible for aspartylglucosaminuria were classified and divided in three groups. PMID: 18992224
    9. Increased AGA plasma activity, although a consistent finding in congenital disorders of glycosylation patients, is not specific to this group of disorders. PMID: 19100247

    顯示更多

    收起更多

  • 相關疾病:
    Aspartylglucosaminuria (AGU)
  • 亞細胞定位:
    Lysosome.
  • 蛋白家族:
    Ntn-hydrolase family
  • 數據庫鏈接:

    HGNC: 318

    OMIM: 208400

    KEGG: hsa:175

    STRING: 9606.ENSP00000264595

    UniGene: Hs.207776



主站蜘蛛池模板: 久久久精品人妻一区二区三区蜜桃| 成人网站免费大全日韩国产| 蜜桃av久久久一区二区三区麻豆| 亚洲精品国产一区二区在线观看| 亚洲6080yy久久无码产自国产| 18禁成人网站免费观看| 欧美色就是色| 久久综合九色欧美婷婷| 日本真人边吃奶边做爽电影| 天天av天天翘天天综合网| 国产精品无码久久久久成人影院| 饥渴少妇av无码影片| 国产明星xxxx色视频| 性做久久久久久久久| 人妻熟女αⅴ一区二区三区| 成人亚洲精品久久久久| 四虎影视884a精品国产| 国产精品天天狠天天看| www国产精品内射老师| 日本边添边摸边做边爱喷水| 超级大爆乳奶牛被调教出奶水 | 国产精品成人一区二区不卡| 8x国产精品视频| 一本大道无码日韩精品影视丶| 精品无码日韩一区二区三区不卡| 国产av麻豆天堂亚洲国产av刚刚碰 | 色天天天综合色天天| 亚洲成αv人片在线观看| 国产精品一区二区久久不卡| 少妇厨房愉情理9仑片视频| 欧美猛少妇色xxxxx猛交| 国产很色很黄很大爽的视频| 国产乱色精品成人免费视频| 国产精品色无码av在线观看| 国内精品久久久久久影院8f| 午夜大片免费男女爽爽影院| 骚片av蜜桃精品一区| 成人无码α片在线观看不卡| 亚洲成a人片在线观看无码| 午夜福利视频合集1000| 日韩精品无码免费一区二区三区 |