在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. SUCLA2 Antibody

SUCLA2 Antibody

  • 中文名稱：
    SUCLA2兔多克隆抗體
  • 貨號：
    CSB-PA022917GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    SUCLA2
  • 別名：
    A BETA antibody; A SCS antibody; ATP specific succinyl CoA synthetase subunit beta antibody; ATP specific succinyl CoA synthetase, beta subunit antibody; ATP-specific succinyl-CoA synthetase subunit beta antibody; Mitochondrial succinyl CoA ligase [ADP forming] subunit beta antibody; MTDPS5 antibody; Renal carcinoma antigen NY-REN-39 antibody; Renal carcinoma antigen NYREN39 antibody; SCS betaA antibody; SCS-betaA antibody; SUCB1_HUMAN antibody; Succinate CoA ligase (ADP forming) antibody; Succinate CoA ligase [ADP forming] subunit beta, mitochondrial, succinyl CoA ligase [ADP forming] subunit beta, mitochondrial antibody; Succinate CoA ligase ADP forming beta subunit antibody; Succinate CoA ligase beta subunit antibody; Succinyl CoA ligase [ADP-forming] subunit beta, mitochondrial antibody; Succinyl CoA synthetase beta A chain antibody; Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial antibody; Succinyl-CoA synthetase beta-A chain antibody; SUCLA2 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human SUCLA2
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    ATP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of ATP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit.
  • 基因功能參考文獻：
    1. SUCLA2 mutation is associated with Down syndrome and mitochondrial depletion syndrome. PMID: 28749033
    2. The patient's cells lack the SUCLG1 protein, with significantly reduced levels of SUCLA2 and SUCLG2 protein PMID: 27484306
    3. Sucla2 is related to the developmental stages of mouse spermatogenesis. Knockdown of Sucla2 decreases the viability of mouse spermatocytes by inducing apoptosis via decreased mitochondrial function of the cells. PMID: 27766610
    4. SUCLA2 mutations should be analyzed in patients with slowly progressive encephalomyopathy, even in the absence of methylmalonic aciduria or mitochondrial DNA depletion. PMID: 24986829
    5. This study demonstrated that SUCLA2 is expressed exclusively in neurons in the human cerebral cortex. PMID: 24085565
    6. Identification of a novel mutation in SUCLA2 in two cousins affected with encephalomyopathy, is reported. PMID: 23759946
    7. A novel homozygous mutation in SUCLA2 gene has been associated with severe mitochondrial encephalomyopathies in two Italian siblings. PMID: 23010432
    8. X-linked sideroblastic anemia due to carboxyl-terminal ALAS2 mutations that cause loss of binding to the beta-subunit of succinyl-CoA synthetase (SUCLA2). PMID: 22740690
    9. Mitochondrial DNA depletion, encephalomyopathic form, with methylmalonic aciduria is associated with mutations in SUCLA2, the gene encoding a beta subunit of succinate-CoA ligase. PMID: 19526370
    10. Deficiency of SUCLA2 is associated with encephalomyopathy and mitochondrial DNA depletion. PMID: 15877282

    顯示更多

    收起更多

  • 相關疾病：
    Mitochondrial DNA depletion syndrome 5 (MTDPS5)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    Succinate/malate CoA ligase beta subunit family, ATP-specific subunit beta subfamily
  • 組織特異性：
    Widely expressed. Not expressed in liver and lung.
  • 數據庫鏈接：

    HGNC: 11448

    OMIM: 603921

    KEGG: hsa:8803

    STRING: 9606.ENSP00000367923

    UniGene: Hs.743361



主站蜘蛛池模板： 在线观看无码不卡av中文| 蜜臀av99无码精品国产专区| 狠狠色丁香婷婷综合尤物| 欧美性生交xxxxx无码久久久 | 露脸叫床粗话东北少妇| 免费做爰猛烈吃奶摸视频在线观看| 手机在线看永久av片免费| 强开小婷嫩苞又嫩又紧视频 | 国产一区二区三区精品视频| 亚洲精品色午夜无码专区日韩| 性久久久久久| 成人国产mv免费视频| 337p亚洲日本中国大胆69| 国产成人无码激情视频| 波多野结衣初尝黑人| 肥老熟妇伦子伦456视频| 亚洲∧v久久久无码精品| 精品麻豆丝袜高跟鞋av| 久久亚洲一区二区三区舞蹈| 亚洲欧美中文高清在线专区 | 久久国产中文娱乐网| 天堂网在线最新版www资源网| 亚洲va综合va国产产va中文| 久久久无码精品国产一区| 日韩人妻无码中文字幕视频| 熟女人妻水多爽中文字幕| 日本十八禁视频无遮挡| 国产精品白浆在线观看免费 | 伊人亚洲综合影院首页| 日产精品一卡2卡三卡4乱码| 中国6一12呦女精品| 国产精品你懂的在线播放| 国产在线精品一区二区夜色| 美女露出奶头扒开尿口视频直播| 国产电影一区二区三区| 狠狠精品干练久久久无码中文字幕| 亚洲成av人片无码bt种子下载| 高潮好爽视频在线观看| 最近的中文字幕在线看视频 | 久久精品中文闷骚内射| 国产午夜aaaaa片在线影院 |