在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. SUCLA2 Antibody

SUCLA2 Antibody

  • 中文名稱：
    SUCLA2兔多克隆抗體
  • 貨號：
    CSB-PA868398ESR1HU
  • 規格：
    ￥440
  • 圖片：
    • Western blot
      All lanes: SUCLA2 antibody at 1.75µg/ml
      Lane 1: Hela whole cell lysate
      Lane 2: Jurkat whole cell lysate
      Lane 3: A549 whole cell lysate
      Lane 4: 293T whole cell lysate
      Lane 5: HepG2 whole cell lysate
      Secondary
      Goat polyclonal to rabbit IgG at 1/10000 dilution
      Predicted band size: 51, 49 kDa
      Observed band size: 51 kDa
    • Immunohistochemistry of paraffin-embedded human ovarian cancer using CSB-PA868398ESR1HU at dilution of 1:100
    • Immunohistochemistry of paraffin-embedded human kidney tissue using CSB-PA868398ESR1HU at dilution of 1:100
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) SUCLA2 Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    SUCLA2
  • 別名：
    A BETA antibody; A SCS antibody; ATP specific succinyl CoA synthetase subunit beta antibody; ATP specific succinyl CoA synthetase, beta subunit antibody; ATP-specific succinyl-CoA synthetase subunit beta antibody; Mitochondrial succinyl CoA ligase [ADP forming] subunit beta antibody; MTDPS5 antibody; Renal carcinoma antigen NY-REN-39 antibody; Renal carcinoma antigen NYREN39 antibody; SCS betaA antibody; SCS-betaA antibody; SUCB1_HUMAN antibody; Succinate CoA ligase (ADP forming) antibody; Succinate CoA ligase [ADP forming] subunit beta, mitochondrial, succinyl CoA ligase [ADP forming] subunit beta, mitochondrial antibody; Succinate CoA ligase ADP forming beta subunit antibody; Succinate CoA ligase beta subunit antibody; Succinyl CoA ligase [ADP-forming] subunit beta, mitochondrial antibody; Succinyl CoA synthetase beta A chain antibody; Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial antibody; Succinyl-CoA synthetase beta-A chain antibody; SUCLA2 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial protein (1-180AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    Non-conjugated
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA, WB, IHC
  • 推薦稀釋比：
    Application Recommended Dilution
    WB 1:1000-1:5000
    IHC 1:20-1:200
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    ATP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of ATP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit.
  • 基因功能參考文獻：
    1. SUCLA2 mutation is associated with Down syndrome and mitochondrial depletion syndrome. PMID: 28749033
    2. The patient's cells lack the SUCLG1 protein, with significantly reduced levels of SUCLA2 and SUCLG2 protein PMID: 27484306
    3. Sucla2 is related to the developmental stages of mouse spermatogenesis. Knockdown of Sucla2 decreases the viability of mouse spermatocytes by inducing apoptosis via decreased mitochondrial function of the cells. PMID: 27766610
    4. SUCLA2 mutations should be analyzed in patients with slowly progressive encephalomyopathy, even in the absence of methylmalonic aciduria or mitochondrial DNA depletion. PMID: 24986829
    5. This study demonstrated that SUCLA2 is expressed exclusively in neurons in the human cerebral cortex. PMID: 24085565
    6. Identification of a novel mutation in SUCLA2 in two cousins affected with encephalomyopathy, is reported. PMID: 23759946
    7. A novel homozygous mutation in SUCLA2 gene has been associated with severe mitochondrial encephalomyopathies in two Italian siblings. PMID: 23010432
    8. X-linked sideroblastic anemia due to carboxyl-terminal ALAS2 mutations that cause loss of binding to the beta-subunit of succinyl-CoA synthetase (SUCLA2). PMID: 22740690
    9. Mitochondrial DNA depletion, encephalomyopathic form, with methylmalonic aciduria is associated with mutations in SUCLA2, the gene encoding a beta subunit of succinate-CoA ligase. PMID: 19526370
    10. Deficiency of SUCLA2 is associated with encephalomyopathy and mitochondrial DNA depletion. PMID: 15877282

    顯示更多

    收起更多

  • 相關疾病：
    Mitochondrial DNA depletion syndrome 5 (MTDPS5)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    Succinate/malate CoA ligase beta subunit family, ATP-specific subunit beta subfamily
  • 組織特異性：
    Widely expressed. Not expressed in liver and lung.
  • 數據庫鏈接：

    HGNC: 11448

    OMIM: 603921

    KEGG: hsa:8803

    STRING: 9606.ENSP00000367923

    UniGene: Hs.743361



主站蜘蛛池模板： 国产在线无码一区二区三区视频| 亚洲a∨精品一区二区三区| 精品久久久久久中文字幕202| 日本边添边摸边做边爱的网站| 熟妇人妻无码中文字幕老熟妇 | 成人午夜特黄aaaaa片男男| 日本免费大黄在线观看| 国产精品igao视频网网址| 色欲色香天天天综合网站| 少妇被粗大的猛进出69影院| 狠狠色噜噜狠狠狠狠777米奇小说| 国产麻豆一精品一av一免费| 成人亚洲精品久久久久| 国产精品久久久久久免费软件 | 日日躁夜夜躁狠狠躁超碰97| 日韩在线永久免费播放| 人妻熟女一区二区aⅴ水野朝阳| 国产精品人成视频免费播放| 国产人妻丰满熟妇嗷嗷叫 | 暴力强奷在线播放无码| 国产人妻精品久久久久野外| 亚洲一区无码中文字幕乱码| 国产福利无码一区在线| 亚洲a无码综合a国产av中文| 人妻少妇精品无码专区二区| 暖暖的在线观看日本社区| 亚洲aⅴ综合av国产八av| 国产露脸150部国语对白| 伊人色综合久久天天| 亚洲欧洲自偷自拍图片| 99亚洲乱人伦aⅴ精品| 人妻丰满熟妞av无码区| 强迫大乳人妻中文字幕| 亚洲免费视频免在线观看| 无码粉嫩虎白一线天在线观看| 香蕉人妻av久久久久天天| 中文字幕无码精品三级在线电影 | 亚洲制服丝袜自拍中文字幕| 精品久久久无码中文字幕 | 亚洲第一无码精品立川理惠| 亚洲色欲www综合网|