在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. SGCB Antibody, FITC conjugated

SGCB Antibody, FITC conjugated

  • 中文名稱：
    SGCB兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA618082LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) SGCB Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    SGCB
  • 別名：
    43 kDa dystrophin associated glycoprotein antibody; 43 kDa dystrophin-associated glycoprotein antibody; 43DAG antibody; A3b antibody; Beta SG antibody; Beta-sarcoglycan antibody; Beta-SG antibody; dystrophin-associated glycoprotein, 43-kD antibody; LGMD2E antibody; Limb girdle muscular dystrophy 2E (non linked families) antibody; Sarcoglycan beta antibody; sarcoglycan, beta (43kDa dystrophin-associated glycoprotein) antibody; SGC antibody; SGCB antibody; SGCB_HUMAN antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Beta-sarcoglycan protein (124-219AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix.
  • 基因功能參考文獻：
    1. This study demonstrated that LGMD2E is the most common type of sarcoglycanopathies in the Iranian population. PMID: 28687063
    2. Clinical severity of limb-girdle muscular dystrophy type 2Emay be predicted by SGCB gene mutation and sarcoglycan protein expression. PMID: 25862795
    3. Defective assembly of sarcoglycan complex in patients with beta-sarcoglycan gene mutations PMID: 12060343
    4. beta-sarcoglycan and SPATA18 may have a role in limb-girdle muscular dystrophy type 2E PMID: 16088906
    5. While the quantity of beta-sarcoglycan was nearly normal in the limb girdle muscular dystrophy (LGMD)2E carrier, the levels of dysferlin protein were reduced to 50% of controls in the carriers of LGMD2B. PMID: 16934466
    6. These data suggest that formation of the beta-delta-core may promote the export and deposition of sarcoglycan subcomplexes at the plasma membrane, and therefore identifies a mechanism for sarcoglycan transport. PMID: 17036316
    7. The limb-girdle muscular dystrophy patients with beta-sarcoglycan deficient LGMD2E do not enable an accurate prediction of the genotype. PMID: 18996010

    顯示更多

    收起更多

  • 相關疾病：
    Limb-girdle muscular dystrophy 2E (LGMD2E)
  • 亞細胞定位：
    Cell membrane, sarcolemma; Single-pass type II membrane protein. Cytoplasm, cytoskeleton.
  • 蛋白家族：
    Sarcoglycan beta/delta/gamma/zeta family
  • 組織特異性：
    Highest expression in heart and skeletal muscle. Low expression in brain, kidney, placenta, pancreas and lung. High expression in fetal brain. Also found in fetal lung, kidney and liver.
  • 數據庫鏈接：

    HGNC: 10806

    OMIM: 600900

    KEGG: hsa:6443

    STRING: 9606.ENSP00000370839

    UniGene: Hs.438953



主站蜘蛛池模板： 免费拍拍拍网站| 亚洲 日韩 国产 有码 不卡| 男人猛躁进女人免费播放| 久久久久久亚洲精品不卡| 久久人人爽人人爽人人片ⅴ| 中文字幕久久久久人妻中出| 午夜人性色福利无码视频在线观看| 无码里番纯肉h在线网站| 在线天堂中文在线资源网| 国产高清无套内谢| 亚洲日本va在线视频观看| 黑人大荫道bbwbbb高潮潮喷| 人妻夜夜爽天天爽三区| 亚洲a成人无码网站在线| 欧洲专线一区二区三区| 99国产精品久久久久久久成人热| 少妇厨房愉情理9仑片视频| 激情综合色五月六月婷婷| 国产产在线精品亚洲aavv| 亚欧免费无码aⅴ在线观看| 国产亚洲精久久久久久无码77777| 边啃奶头边躁狠狠躁玩爽在水里面| 嫩草国产露脸精品国产软件| 试看120分钟做受小视频| 国内精品久久久久影院嫩草| 天天爽天天狠久久久综合麻豆| 夜夜高潮夜夜爽夜夜爱爱一区 | 亚洲人成色7777在线观看| 好男人日本社区www| 成人亚洲欧美丁香在线观看| 婷婷色婷婷开心五月四房播播| 日韩人妻无码一区二区三区久久99 | 亚洲色爱免费观看视频| 亚洲 中文字幕 日韩 无码| 欧美两根一起进3p做受视频| 亚洲孰妇无码av在线播放| 欧美人与牲动交xxxx| 亚洲精品乱码久久久久久不卡| 久久精品亚洲国产av老鸭网| 日韩不卡1卡2卡三卡2021免费 | 久久99精品国产麻豆婷婷|