在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. PREPL Antibody, FITC conjugated

PREPL Antibody, FITC conjugated

  • 中文名稱：
    PREPL兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA018665LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) PREPL Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    PREPL
  • 別名：
    PPCEL_HUMAN antibody; prepl antibody; Prolyl endopeptidase-like antibody; Prolylendopeptidase-like antibody; putative prolyl oligopeptidase antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Prolyl endopeptidase-like protein (604-699AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Serine peptidase whose precise substrate specificity remains unclear. Does not cleave peptides after a arginine or lysine residue. Regulates trans-Golgi network morphology and sorting by regulating the membrane binding of the AP-1 complex. May play a role in the regulation of synaptic vesicle exocytosis.
  • 基因功能參考文獻：
    1. we report the first homozygous PREPL point mutation in a girl with typical PREPL deficiency. This syndrome should be considered in the differential diagnosis of hypotonic neonates exhibiting myasthenic symptoms, hyperphagia, and various degrees of ID. PMID: 29483676
    2. Deletion of PREPL is associated with Hypotonia-cystinuria syndrome. PMID: 23794250
    3. Two novel deletions encompassing the SLC3A1 and PREPL genes have been identified in unrelated hypotonia-cystinuria syndrome patients. PMID: 22796000
    4. description of L-leucine transport into bladder carcinoma cells PMID: 12225859
    5. A 638-residue variant of PREPL, PREPL A, was identifiied, expressed in Escherichia coli and purified; its secondary structure was similar to that of oligopeptidase B. PMID: 16143824
    6. Deletion of PREPL, a gene encoding a putative serine oligopeptidase, in patients with hypotonia-cystinuria syndrome. PMID: 16385448
    7. Deletion of the gene results in hypotonia at birth, failure to thrive and growth hormone deficiency PMID: 16913837
    8. a deletion of PREPL causes atypical hypotonia-cystinuria syndrome PMID: 18234729

    顯示更多

    收起更多

  • 相關疾病：
    Hypotonia-cystinuria syndrome (HCS); Myasthenic syndrome, congenital, 22 (CMS22)
  • 亞細胞定位：
    Cytoplasm, cytosol. Golgi apparatus, trans-Golgi network. Cytoplasm, cytoskeleton. Golgi apparatus. Nucleus.
  • 蛋白家族：
    Peptidase S9A family
  • 組織特異性：
    Expressed in pyramidal neurons of the temporal cortex and neocortex (at protein level). Widely expressed. Expressed at higher level in brain, skeletal muscle, heart and kidney. Expressed at the endplates in the neuromuscular junction.
  • 數據庫鏈接：

    HGNC: 30228

    OMIM: 606407

    KEGG: hsa:9581

    STRING: 9606.ENSP00000260648

    UniGene: Hs.444349



主站蜘蛛池模板： 熟妇人妻激情偷爽文| 色喜国模李晴超大尺度 | 国产性猛交╳xxx乱大交| 中文www天堂| 在线精品国产大象香蕉网| 欧美大荫蒂毛茸茸视频| 国产精品18久久久久久vr| 国产乱人伦在线播放| 国产av人人夜夜澡人人爽| 日本熟妇hdsex视频| 久久成人伊人欧洲精品| 夜夜高潮夜夜爽夜夜爱| 少妇荡乳情欲办公室456视频| 精品国内自产拍在线播放观看| 日韩av高潮喷水在线观看| 精品亚洲国产成人av在线小说| 热99re久久精品| 一本色综合网久久| 国精品午夜福利视频| 国产美女遭强高潮网站观看| 国产精品偷伦视频免费观看了| 国产做无码视频在线观看| 高清破外女出血av毛片| 最新国产精品久久精品| 国产免费一区二区三区在线观看| 少妇系列之白嫩人妻| 中文成人无码精品久久久不卡| 国产午睡沙发被弄醒完整版| 天堂中文在线www天堂在线| 99国产精品白浆在线观看免费 | 亚洲乱码中文字幕小综合| 无码人妻丰满熟妇区96| 狠狠躁夜夜躁人人爽天天不卡 | 无码人妻久久一区二区三区蜜桃| 久久综合九色综合欧美婷婷| 精品三级久久久久电影网| 夜夜高潮夜夜爽夜夜爱| 天堂国产一区二区三区| 国产如狼似虎富婆找强壮黑人| 国产无套粉嫩白浆在线观看 | 免费看成人aa片无码视频|