在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

PREPL Antibody, Biotin conjugated

  • 中文名稱:
    PREPL兔多克隆抗體, Biotin偶聯
  • 貨號:
    CSB-PA018665LD01HU
  • 規格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) PREPL Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    PREPL
  • 別名:
    PPCEL_HUMAN antibody; prepl antibody; Prolyl endopeptidase-like antibody; Prolylendopeptidase-like antibody; putative prolyl oligopeptidase antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Prolyl endopeptidase-like protein (604-699AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Biotin
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Serine peptidase whose precise substrate specificity remains unclear. Does not cleave peptides after a arginine or lysine residue. Regulates trans-Golgi network morphology and sorting by regulating the membrane binding of the AP-1 complex. May play a role in the regulation of synaptic vesicle exocytosis.
  • 基因功能參考文獻:
    1. we report the first homozygous PREPL point mutation in a girl with typical PREPL deficiency. This syndrome should be considered in the differential diagnosis of hypotonic neonates exhibiting myasthenic symptoms, hyperphagia, and various degrees of ID. PMID: 29483676
    2. Deletion of PREPL is associated with Hypotonia-cystinuria syndrome. PMID: 23794250
    3. Two novel deletions encompassing the SLC3A1 and PREPL genes have been identified in unrelated hypotonia-cystinuria syndrome patients. PMID: 22796000
    4. description of L-leucine transport into bladder carcinoma cells PMID: 12225859
    5. A 638-residue variant of PREPL, PREPL A, was identifiied, expressed in Escherichia coli and purified; its secondary structure was similar to that of oligopeptidase B. PMID: 16143824
    6. Deletion of PREPL, a gene encoding a putative serine oligopeptidase, in patients with hypotonia-cystinuria syndrome. PMID: 16385448
    7. Deletion of the gene results in hypotonia at birth, failure to thrive and growth hormone deficiency PMID: 16913837
    8. a deletion of PREPL causes atypical hypotonia-cystinuria syndrome PMID: 18234729

    顯示更多

    收起更多

  • 相關疾病:
    Hypotonia-cystinuria syndrome (HCS); Myasthenic syndrome, congenital, 22 (CMS22)
  • 亞細胞定位:
    Cytoplasm, cytosol. Golgi apparatus, trans-Golgi network. Cytoplasm, cytoskeleton. Golgi apparatus. Nucleus.
  • 蛋白家族:
    Peptidase S9A family
  • 組織特異性:
    Expressed in pyramidal neurons of the temporal cortex and neocortex (at protein level). Widely expressed. Expressed at higher level in brain, skeletal muscle, heart and kidney. Expressed at the endplates in the neuromuscular junction.
  • 數據庫鏈接:

    HGNC: 30228

    OMIM: 606407

    KEGG: hsa:9581

    STRING: 9606.ENSP00000260648

    UniGene: Hs.444349



主站蜘蛛池模板: 92精品成人国产在线观看| 97人妻熟女成人免费视频色戒| 一本大道东京热无码| 无套内谢孕妇毛片免费看| 人妻熟女αⅴ一区二区三区| 亚洲成av人在线播放无码| 亚洲2021av天堂手机版| 久久久噜噜噜久久熟女aa片| 人人爽天天碰狠狠添| 67194熟妇在线直接进入| 狠狠躁18三区二区一区| 无码福利一区二区三区| 波多野结衣av一区二区全免费观看 | 麻豆熟妇人妻xxxxxx| 岛国无码av不卡一区二区| 无码国产成人午夜电影在线观看 | 久久国产成人精品国产成人亚洲| 九个美女露脸撒尿嘘嘘视频| 中文字幕人妻av一区二区| 天堂资源在线官网| 法国伦理少妇愉情| 一区二区三区人妻无码| 国产亚洲视频在线观看播放| 亚洲2020天天堂在线观看 | 日本看片一二三区高清| 无码精品人妻一区二区三区av| 国产精品丝袜高跟鞋| 蜜臀av在线播放| 精品人妻无码一区二区三区| 极品少妇扒开粉嫩小泬视频| 免费看小12萝裸体视频国产| 亚洲毛片多多影院| 国产婷婷色综合av蜜臀av| 国产精品天干天干综合网| 国产乱人伦av在线a更新| 久久久无码精品国产一区| 日韩吃奶摸下aa片免费观看| 国产免费mv大片人人电影播放器| 国产极品美女到高潮| 成在人线av无码免费漫画| 国产精品无码av不卡顿 |