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NDUFA9 Antibody

  • 中文名稱:
    NDUFA9兔多克隆抗體
  • 貨號:
    CSB-PA912628
  • 規格:
    ¥1100
  • 圖片:
    • The image on the left is immunohistochemistry of paraffin-embedded Human colon cancer tissue using CSB-PA912628(NDUFA9 Antibody) at dilution 1/30, on the right is treated with fusion protein. (Original magnification: ×200)
    • Gel: 8%SDS-PAGE, Lysate: 40 μg, Lane 1-2: Mouse heart tissue, Mouse kidney tissue, Primary antibody: CSB-PA912628(NDUFA9 Antibody) at dilution 1/400, Secondary antibody: Goat anti rabbit IgG at 1/8000 dilution, Exposure time: 10 seconds
  • 其他:

產品詳情

  • Uniprot No.:
  • 基因名:
  • 別名:
    CI-39kD antibody; Complex I subunit NDUFA9 antibody; Complex I-39kD antibody; mitochondrial antibody; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9 antibody; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9 mitochondrial antibody; NADH Ubiquinone Oxidoreductase 1 alpha subcomplex 9 antibody; NADH-ubiquinone oxidoreductase 39 kDa subunit antibody; NDUA9_HUMAN antibody; NDUFA9 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse
  • 免疫原:
    Fusion protein of Human NDUFA9
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen affinity purification
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    -20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB,IHC
  • 推薦稀釋比:
    Application Recommended Dilution
    ELISA 1:2000-1:5000
    WB 1:500-1:2000
    IHC 1:50-1:200
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Required for proper complex I assembly. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone.
  • 基因功能參考文獻:
    1. NDUFA9 protein is essential for stabilizing the junction between membrane and matrix arms of complex I. PMID: 23223238
    2. A pathogenic mutation was found in the complex I subunit encoding the NDUFA9 gene, changing a highly conserved arginine at position 321 to proline PMID: 22114105
    3. Study identifies mitochondrial transit peptide and determines mature protein cleavage site in cow ortholog. PMID: 1832859
  • 相關疾?。?/div>
    Leigh syndrome (LS)
  • 亞細胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Complex I NDUFA9 subunit family
  • 數據庫鏈接:

    HGNC: 7693

    OMIM: 256000

    KEGG: hsa:4704

    STRING: 9606.ENSP00000266544

    UniGene: Hs.75227



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