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NDUFA9 Antibody

  • 中文名稱:
    NDUFA9兔多克隆抗體
  • 貨號:
    CSB-PA937714
  • 規格:
    ¥2024
  • 圖片:
    • Western blot analysis of extracts from HeLa cells, using NDUFA9 antibody.
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) NDUFA9 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Synthesized peptide derived from internal of Human NDUFA9.
  • 免疫原種屬:
    Homo sapiens (Human)
  • 克隆類型:
    Polyclonal
  • 純化方式:
    The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:500-1:3000
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Required for proper complex I assembly. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone.
  • 基因功能參考文獻:
    1. NDUFA9 protein is essential for stabilizing the junction between membrane and matrix arms of complex I. PMID: 23223238
    2. A pathogenic mutation was found in the complex I subunit encoding the NDUFA9 gene, changing a highly conserved arginine at position 321 to proline PMID: 22114105
    3. Study identifies mitochondrial transit peptide and determines mature protein cleavage site in cow ortholog. PMID: 1832859
  • 相關疾病:
    Leigh syndrome (LS)
  • 亞細胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Complex I NDUFA9 subunit family
  • 數據庫鏈接:

    HGNC: 7693

    OMIM: 256000

    KEGG: hsa:4704

    STRING: 9606.ENSP00000266544

    UniGene: Hs.75227



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