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Your Good Partner in Biology Research

MRPL3 Antibody

  • 中文名稱:
    MRPL3兔多克隆抗體
  • 貨號(hào):
    CSB-PA014836GA01HU
  • 規(guī)格:
    ¥3,900
  • 其他:

產(chǎn)品詳情

  • Uniprot No.:
  • 基因名:
    MRPL3
  • 別名:
    39S ribosomal protein L3 antibody; 39S ribosomal protein L3 mitochondrial antibody; COXPD9 antibody; L3mt antibody; Mitochondrial 39S ribosomal protein L3 antibody; Mitochondrial 60S ribosomal protein L3 antibody; mitochondrial antibody; mitochondrial ribosomal protein antibody; Mitochondrial ribosomal protein L3 antibody; MRL3 antibody; MRP-L3 antibody; MRPL3 antibody; RM03_HUMAN antibody; RPML3 antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human,Mouse,Rat
  • 免疫原:
    Human MRPL3
  • 免疫原種屬:
    Homo sapiens (Human)
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen Affinity purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產(chǎn)品提供形式:
    Liquid
  • 應(yīng)用范圍:
    ELISA,WB,IHC
  • Protocols:
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 基因功能參考文獻(xiàn):
    1. Found MRPL3 S75N variant is probably a rare cause of Tourette syndrome/chronic tic phenotype in Chinese Han patients. PMID: 22507240
    2. the first mutation in large mitochondrial ribosomal protein MRPL3 in a family of four sibs with hypertrophic cardiomyopathy, psychomotor retardation, and multiple respiratory chain deficiency.(MRPL3) PMID: 21786366
  • 相關(guān)疾病:
    Combined oxidative phosphorylation deficiency 9 (COXPD9)
  • 亞細(xì)胞定位:
    Mitochondrion.
  • 蛋白家族:
    Universal ribosomal protein uL3 family
  • 數(shù)據(jù)庫鏈接:

    HGNC: 10379

    OMIM: 607118

    KEGG: hsa:11222

    STRING: 9606.ENSP00000264995

    UniGene: Hs.205163



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