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MRPL3 Antibody, FITC conjugated

  • 中文名稱:
    MRPL3兔多克隆抗體, FITC偶聯(lián)
  • 貨號:
    CSB-PA014836LC01HU
  • 規(guī)格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) MRPL3 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    MRPL3
  • 別名:
    39S ribosomal protein L3 antibody; 39S ribosomal protein L3 mitochondrial antibody; COXPD9 antibody; L3mt antibody; Mitochondrial 39S ribosomal protein L3 antibody; Mitochondrial 60S ribosomal protein L3 antibody; mitochondrial antibody; mitochondrial ribosomal protein antibody; Mitochondrial ribosomal protein L3 antibody; MRL3 antibody; MRP-L3 antibody; MRPL3 antibody; RM03_HUMAN antibody; RPML3 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human 39S ribosomal protein L3, mitochondrial protein (201-348AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 基因功能參考文獻:
    1. Found MRPL3 S75N variant is probably a rare cause of Tourette syndrome/chronic tic phenotype in Chinese Han patients. PMID: 22507240
    2. the first mutation in large mitochondrial ribosomal protein MRPL3 in a family of four sibs with hypertrophic cardiomyopathy, psychomotor retardation, and multiple respiratory chain deficiency.(MRPL3) PMID: 21786366
  • 相關疾病:
    Combined oxidative phosphorylation deficiency 9 (COXPD9)
  • 亞細胞定位:
    Mitochondrion.
  • 蛋白家族:
    Universal ribosomal protein uL3 family
  • 數據庫鏈接:

    HGNC: 10379

    OMIM: 607118

    KEGG: hsa:11222

    STRING: 9606.ENSP00000264995

    UniGene: Hs.205163



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