在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. MCCC2 Antibody

MCCC2 Antibody

  • 中文名稱：
    MCCC2兔多克隆抗體
  • 貨號：
    CSB-PA013573GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    MCCC2
  • 別名：
    MCCC2 antibody; MCCBMethylcrotonoyl-CoA carboxylase beta chain antibody; mitochondrial antibody; MCCase subunit beta antibody; EC 6.4.1.4 antibody; 3-methylcrotonyl-CoA carboxylase 2 antibody; 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit antibody; 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human MCCC2
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism.
  • 基因功能參考文獻：
    1. Novel mutation in MCCC2 gene was identified in Chinese population. PMID: 25382614
    2. Mutation in 3-methylcrotonyl CoA carboxylase 2 gene is associated with 3-methylcrotonyl-CoA carboxylase deficiency. PMID: 22264772
    3. The amino-termini containing 20 amino acids (MCCbeta) were both necessary and sufficient for targeting. Structural requirements for mitochondrial import were defined by site-directed mutagenesis. PMID: 16023992
    4. The Kd value of soraphen A for the BC domains of human ACC1 and ACC2 is 1 nM. This high binding affinity is mainly due to the extensive interactions between soraphen A and the human biotin carboxylase domain PMID: 17876819
  • 相關疾病：
    3-methylcrotonoyl-CoA carboxylase 2 deficiency (MCC2D)
  • 亞細胞定位：
    Mitochondrion matrix.
  • 蛋白家族：
    AccD/PCCB family
  • 數據庫鏈接：

    HGNC: 6937

    OMIM: 210210

    KEGG: hsa:64087

    STRING: 9606.ENSP00000343657

    UniGene: Hs.604789



主站蜘蛛池模板： 日本人妻人人人澡人人爽| 一边吃奶一边摸做爽视频| 综合网日日天干夜夜久久| 国产av国片偷人妻麻豆| 亚洲一区日韩高清中文字幕亚洲| 亚洲精品综合欧美一区二区三区 | 亚洲高清国产拍精品26u| 亚洲一区二区三区av天堂| 国产99久久久国产精品～～牛| 性色a∨精品高清在线观看| 三级理论中文字幕在线播放| 亲近乱子伦免费视频| 隔壁邻居是巨爆乳寡妇| 精品国际久久久久999| 亚洲色无码专区一区| 色五月丁香六月欧美综合| 久久久无码中文字幕久...| 国产av精品毛片一区二区三区| 亚洲国产成人高清影视| 国产偷窥熟女高潮精品视频| 精品 日韩 国产 欧美 视频| 少妇人妻上班偷人精品视频| 久久精品女同亚洲女同| 加勒比无码一区二区三区| 欧美精品18videosex性欧美| 日韩精品一区二区大桥未久| 中文无码人妻有码人妻中文字幕 | 国精品无码人妻一区二区三区| 日本高清www午色夜在线视频 | 大乳丰满人妻中文字幕日本| 99热这里只有精品最新地址获取| 天天天天噜在线视频| 国产亚洲精品字幕在线观看| 国产成人人人97超碰超爽8| 国产一区二区三区在线电影| 国产日产高清欧美一区| 亚洲日韩乱码久久久久久| 国产精品亚洲а∨天堂免下载| 在线a亚洲v天堂网2018| 日韩精品久久无码中文字幕| 久久久久国产精品人妻aⅴ院|