在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. DNAH5 Antibody, Biotin conjugated

DNAH5 Antibody, Biotin conjugated

  • 中文名稱：
    DNAH5兔多克隆抗體, Biotin偶聯(lián)
  • 貨號：
    CSB-PA819476LD01HU
  • 規(guī)格：
    ￥880
  • 其他：

產(chǎn)品詳情

  • 產(chǎn)品名稱：
    Rabbit anti-Homo sapiens (Human) DNAH5 Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    DNAH5
  • 別名：
    axonemal antibody; Axonemal beta dynein heavy chain 5 antibody; Ciliary dynein heavy chain 5 antibody; DNAH 5 antibody; Dnah5 antibody; DNAHC5 antibody; DYH5_HUMAN antibody; Dynein heavy chain 5 antibody; Dynein heavy chain 5; axonemal antibody; HL1 antibody; KIAA1603 antibody
  • 宿主：
    Rabbit
  • 反應(yīng)種屬：
    Human
  • 免疫原：
    Recombinant Human Dynein heavy chain 5, axonemal protein (2364-2560AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標(biāo)記方式：
    Biotin
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式：
    Liquid
  • 應(yīng)用范圍：
    ELISA
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評價

靶點詳情

  • 功能：
    Force generating protein of respiratory cilia. Produces force towards the minus ends of microtubules. Dynein has ATPase activity; the force-producing power stroke is thought to occur on release of ADP. Required for structural and functional integrity of the cilia of ependymal cells lining the brain ventricles.
  • 基因功能參考文獻(xiàn)：
    1. A novel mutation causing primary ciliary dyskinesia was found in Japanese patients. PMID: 28939216
    2. to the best of our knowledge, the first reported case of PCD caused by the DNAH5 mutation in a Japanese patient. PMID: 27779714
    3. These findings demonstrated that new DNAH5 mutations could be used for molecular diagnosis of Kartagener syndrome, providing families with genetic counseling and prenatal diagnosis. PMID: 27988889
    4. The mutation of p.Glu2610Gly in DNAH5 is novel. PMID: 24912412
    5. In chronic obstructive pulmonary disease, total lung capacity was associated with a SNP in DNAH5. PMID: 25134640
    6. A novel mutation in DNAH5 (c. 8030G>A) is identified in a Han Chinese family with chronic rhinosinusitis and primary ciliary dyskinesia. PMID: 24150548
    7. DNAH5 (rs2277046) is associated with single nucleotide polymorphisms in Korean patients, either non-segmental or segmental type. PMID: 23678272
    8. DNAH5 is the cause of primary ciliary dyskinesia in two siblings in a nuclear family as identified by whole genome sequencing. PMID: 20220176
    9. immunofluorescence studies of respiratory epithelial cells with secondary ciliary dyskinesia identified in vitro and in vivo normal axonemal DNAH5 localization PMID: 16492982
    10. DNAH5 is frequently mutated in patients with primary ciliary dyskinesia exhibiting outer dynein arm defects and mutations cluster in five exons. PMID: 16627867
    11. Male carriers of the mutations always exhibit asthenozoospermia, whereas female carriers manifest no alterations in either fertility or pulmonary clearance. PMID: 18492703
    12. Two dynein genes, encoding ODA intermediate chain (DNAI1) and heavy chain (DNAH5), have been seen to be mutated in approximately 30-38% of the families PMID: 19300264
    13. Although genetic alterations remain to be identified in most patients, DNAH5 is to date the main PCD gene. PMID: 19357118
    14. Two "major" genes, DNAI1 and DNAH5, underlie PCD in nearly half of the patients with ODA defects PMID: 19410201

    顯示更多

    收起更多

  • 相關(guān)疾病：
    Ciliary dyskinesia, primary, 3 (CILD3)
  • 亞細(xì)胞定位：
    Cytoplasm, cytoskeleton, cilium axoneme.
  • 蛋白家族：
    Dynein heavy chain family
  • 組織特異性：
    Expressed in airway epithelial cells (at protein level). Not detected in spermatozoa (at protein level).
  • 數(shù)據(jù)庫鏈接：

    HGNC: 2950

    OMIM: 603335

    KEGG: hsa:1767

    STRING: 9606.ENSP00000265104

    UniGene: Hs.212360



主站蜘蛛池模板： 无码三级av电影在线观看| 曰本丰满熟妇xxxx性| 国产亚洲人成a在线v网站| 爆爽久久久一区二区又大又黄又嫩 | 999久久久精品国产消防器材| 女人被狂躁高潮啊的视频在线看| 国产无遮挡又黄又爽在线观看 | 熟妇玩小男视频在线| av性色av久久无码ai换脸| 欧美另类videossexo高潮| 亚洲欧美综合区丁香五月小说| 欧美乱码伦视频免费| 他掀开裙子把舌头伸进去添视频| 强行糟蹋人妻hd中文| 久久久久久国产精品免费免费男同 | 无套内射在线无码播放| 国产精品成人永久在线四虎| 六月丁香亚洲综合在线视频 | 变态另类先锋影音| 图片区小说区av区| 国产成人拍精品视频午夜网站| 尹人香蕉久久99天天拍久女久| 国产亚洲精品久久yy5099| 又爽又黄又无遮挡的激情视频| 少妇av射精精品蜜桃专区| 国模欢欢炮交啪啪150| 日本毛茸茸的丰满熟妇| 欧美精品人人做人人爱视频| 业余 自由 性别 成熟偷窥| 亚洲最大的imax影院| 欧美伦费免费全部午夜最新| 毛片内射-百度| 国产欧美一区二区三区在线看| 老湿机69福利区18禁网站| 色94色欧美sute亚洲线路一| 精品国产乱码久久久久久口爆| 国内揄拍国内精品少妇国语| 亚洲国产成人久久综合同性 | 人人妻人人澡人人爽人人精品浪潮| 久久亚洲中文字幕精品一区| 妲己丰满人熟妇大尺度人体艺|