在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

CHST3 Antibody

  • 中文名稱:
    CHST3兔多克隆抗體
  • 貨號:
    CSB-PA005409GA01HU
  • 規格:
    ¥3,900
  • 其他:

產品詳情

  • Uniprot No.:
  • 基因名:
    CHST3
  • 別名:
    C6ST 1 antibody; C6ST antibody; C6ST-1 antibody; C6ST1 antibody; Carbohydrate (chondroitin 6) sulfotransferase 3 antibody; Carbohydrate sulfotransferase 3 antibody; Chondroitin 6 O sulfotransferase 1 antibody; Chondroitin 6 sulfotransferase antibody; Chondroitin 6-O-sulfotransferase 1 antibody; Chondroitin 6-sulfotransferase antibody; CHST 3 antibody; Chst3 antibody; CHST3_HUMAN antibody; Galactose/N acetylglucosamine/N acetylglucosamine 6 O sulfotransferase 0 antibody; Galactose/N-acetylglucosamine/N-acetylglucosamine 6-O-sulfotransferase 0 antibody; GST 0 antibody; GST-0 antibody; GST0 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse,Rat
  • 免疫原:
    Human CHST3
  • 免疫原種屬:
    Homo sapiens (Human)
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen Affinity purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB,IHC
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Sulfotransferase that utilizes 3'-phospho-5'-adenylyl sulfate (PAPS) as sulfonate donor to catalyze the transfer of sulfate to position 6 of the N-acetylgalactosamine (GalNAc) residue of chondroitin. Chondroitin sulfate constitutes the predominant proteoglycan present in cartilage and is distributed on the surfaces of many cells and extracellular matrices. Catalyzes with a lower efficiency the sulfation of Gal residues of keratan sulfate, another glycosaminoglycan. Can also catalyze the sulfation of the Gal residues in sialyl N-acetyllactosamine (sialyl LacNAc) oligosaccharides. May play a role in the maintenance of naive T-lymphocytes in the spleen.
  • 基因功能參考文獻:
    1. We describe three consanguineous Indian families with a distinct form of spondyloepiphyseal dysplasia (SED Omani type). It is an autosomal recessive disorder due to mutation in CHST3 gene. PMID: 27753269
    2. A novel CHST3 allele associated with spondyloepiphyseal dysplasia and hearing loss has been described in a consanguineous Pakistani pedigree. PMID: 26572954
    3. Sequencing of CHST3 detected a previously unreported homozygous duplication c.407_426dup (p.Thr143Cysfs*80). The mutation is predicted to lead to frameshift and introduction of a premature stopcodon. PMID: 24300290
    4. expression of CHST3 mRNA was significantly reduced in the intervertebral disc cells of subjects carrying the A allele of rs4148941 PMID: 24216480
    5. The results of this study indicated that the critical period for cortical plasticity is regulated by the 4S/6S ratio of CSPGs, which determines the maturation of parvalbumin-expressing interneurons. PMID: 22246436
    6. Vertebral changes, normal carpal age, lack of facial flattening, and recessive inheritance are characteristic and distinguishes CHST3 deficiency from other disorders with congenital dislocations. PMID: 20830804
    7. report eight CHST3 mutations in six unrelated individuals who presented at birth with congenital joint dislocations PMID: 18513679
    8. Sulfation of the galactose residues in the glycosaminoglycan-protein linkage region by recombinant human chondroitin 6-O-sulfotransferase-1. PMID: 18697746
    9. homozygous missense mutation (T141M) in exon 3 in all three family members with spondyloepiphyseal dysplasia with cardiac involvement PMID: 19320654

    顯示更多

    收起更多

  • 相關疾病:
    Spondyloepiphyseal dysplasia with congenital joint dislocations (SEDCJD)
  • 亞細胞定位:
    Golgi apparatus membrane; Single-pass type II membrane protein.
  • 蛋白家族:
    Sulfotransferase 1 family, Gal/GlcNAc/GalNAc subfamily
  • 組織特異性:
    Widely expressed in adult tissues. Expressed in heart, placenta, skeletal muscle and pancreas. Also expressed in various immune tissues such as spleen, lymph node, thymus and appendix.
  • 數據庫鏈接:

    HGNC: 1971

    OMIM: 143095

    KEGG: hsa:9469

    STRING: 9606.ENSP00000362207

    UniGene: Hs.158304



主站蜘蛛池模板: 蜜臀av色欲a片无人一区| 国产性生交xxxxx无码| 一本大道东京热无码一区| 性久久久久久| 久久精品国产亚洲一区二区| 国产亚洲精品久久久久9999| 97国产一区二区三区四区久久 | 狠狠色狠狠色综合网| 日日碰狠狠添天天爽| 狠狠色丁香婷婷久久综合| 亚洲色丰满少妇高潮18p| 人妻夜夜爽天天爽三区丁香花 | av无码免费岛国动作片片段欣赏网| 插插插精品亚洲一区| 免费人成在线观看网站| 少妇粉嫩小泬喷水视频| 亚洲色大网站www永久网站| 天堂在线www资源| 制服丝袜中文字幕在线| 亚洲中文字幕无码一久久区 | 久久www成人片免费看| 婷婷射精av这里只有精品| 成 人 色 网 站免费观看| 国产又黄又爽又色的免费| 把腿张开老子臊烂你多p视频 | 精品无码久久久久国产电影| 午夜精品一区二区三区在线视| 丰满少妇被猛烈进入高清播放| 84pao国产成视频永久免费 | 一本热久久sm色国产| 人妻中文无码久热丝袜| 国产清纯白嫩初高生在线观看| 男女一边摸一边做爽爽的免费阅读 | 爽爽午夜影视窝窝看片| 国产黑色丝袜视频在线观看网红| 国产裸体美女永久免费无遮挡| 少妇高潮喷潮久久久影院| 伊人无码一区二区三区| 中文字幕久久精品波多野结百度| 日韩av无码中文字幕| 成人午夜亚洲精品无码区毛片|