在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. AUH Antibody

AUH Antibody

  • 中文名稱：
    AUH兔多克隆抗體
  • 貨號：
    CSB-PA621698ESR2HU
  • 規格：
    ￥440
  • 圖片：
    • Western blot
      All lanes: Methylglutaconyl-CoA hydratase, mitochondrial antibody at 6μg/ml
      Lane 1: Rat brain tissue
      Lane 2: Rat kidney tissue
      Secondary
      Goat polyclonal to rabbit IgG at 1/10000 dilution
      Predicted band size: 36, 33 kDa
      Observed band size: 36 kDa
    • Immunohistochemistry of paraffin-embedded human tonsil tissue using CSB-PA621698ESR2HU at dilution of 1: 100
    • Immunohistochemistry of paraffin-embedded human kidney tissue using CSB-PA621698ESR2HU at dilution of 1: 100
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) AUH Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    AUH
  • 別名：
    AUHMethylglutaconyl-CoA hydratase antibody; mitochondrial antibody; EC 4.2.1.18 antibody; AU-specific RNA-binding enoyl-CoA hydratase antibody; AU-binding protein/enoyl-CoA hydratase antibody; Itaconyl-CoA hydratase antibody; EC 4.2.1.56 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human, Rat
  • 免疫原：
    Recombinant Human Methylglutaconyl-CoA hydratase, mitochondrial protein (68-339AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    Non-conjugated
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA, WB, IHC
  • 推薦稀釋比：
    Application Recommended Dilution
    WB 1:500-1:2000
    IHC 1:20-1:200
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Catalyzes the conversion of 3-methylglutaconyl-CoA to 3-hydroxy-3-methylglutaryl-CoA. Also has itaconyl-CoA hydratase activity by converting itaconyl-CoA into citramalyl-CoA in the C5-dicarboxylate catabolism pathway. The C5-dicarboxylate catabolism pathway is required to detoxify itaconate, a vitamin B12-poisoning metabolite. Has very low enoyl-CoA hydratase activity. Was originally identified as RNA-binding protein that binds in vitro to clustered 5'-AUUUA-3' motifs.
  • 基因功能參考文獻：
    1. AUH localizes to the inner mitochondrial membrane and matrix where it associates with mitochondrial ribosomes and regulates protein synthesis. PMID: 24598254
    2. Phenotypic heterogeneity in two siblings with 3-methylglutaconic aciduria type I caused by a novel deletion of exons 1-3 within the AUH gene. PMID: 21840233
    3. 3-Methylglutaconic aciduria type I is caused by mutations in AUH PMID: 12434311
    4. Human 3-methylglutaconyl-CoA hydratase is identical with RNA-binding protein (AUH); molecular analyses of MGA1 patients show homozygosity or compound heterozygosity for mutations in AUH. PMID: 12655555
    5. Mutation analysis in the AUH gene revealed homozygosity for a novel splice site mutation IVS9-2A>G. We conclude that MGA1 may be associated with fever-associated seizures even in children without delayed psychomotor development. PMID: 15033206
    6. Mutations in the AUH gene are linked to metabolic disease 3-methylglutaconic aciduria type I (MGA1). PMID: 16640564
    7. The AUH trimer dimerizes upon binding to one molecule of a long RNA containing 24 repeats of the AUUU motif, (AUUU)(24)A. PMID: 18831052

    顯示更多

    收起更多

  • 相關疾病：
    3-methylglutaconic aciduria 1 (MGA1)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    Enoyl-CoA hydratase/isomerase family
  • 數據庫鏈接：

    HGNC: 890

    OMIM: 250950

    KEGG: hsa:549

    STRING: 9606.ENSP00000364883

    UniGene: Hs.175905



主站蜘蛛池模板： 欧洲女人性开放免费网站| 中文字幕乱妇无码av在线| 无码专区天天躁天天躁在线| 久久亚洲道色宗和久久| 亚洲乱码中文字幕小综合| 国产农村妇女毛片精品久久| 99热久久这里只有精品| 熟女毛多熟妇人妻在线视频| 午夜免费啪在线观看视频| 午夜精品久久久久久久喷水| 四虎亚洲中文字幕无码永久 | 久久激情五月丁香伊人| 国产精品久久久久久久久久久免费看 | 国产精品麻豆成人av电影艾秋| 国产精品一线二线三线| 又色又爽又黄的gif动态图| 国产午夜免费高清久久影院| 亚洲精品成人网站在线观看| 亚洲精品亚洲人成人网| 国产精品女上位好爽在线| 四虎www永久在线精品| 国产精品av在线| 亚洲一线二线三线写真| 女学生14毛片视频片二毛| 人妻无码精品久久亚瑟影视| 亚洲精品一区二区三区在线| 亚洲国产精品日韩av不卡在线| 日本高清二区视频久二区| 青青草视频在线观看| 精品无人区卡一卡二卡三乱码 | 中国xxx农村性视频| 麻花传媒在线观看免费 | 亚洲高清成人aⅴ片| 日韩亚洲国产高清免费视频| 影音先锋女人av鲁色资源网久久| 色综合久久久久无码专区| 国产 日韩 欧美 视频 制服| 精品无人码麻豆乱码1区2区| 婷婷五月深深久久精品| 色综合亚洲一区二区小说| 插一插射一射视频|