在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. AUH Antibody

AUH Antibody

  • 中文名稱：
    AUH兔多克隆抗體
  • 貨號：
    CSB-PA002451GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    AUH
  • 別名：
    AUHMethylglutaconyl-CoA hydratase antibody; mitochondrial antibody; EC 4.2.1.18 antibody; AU-specific RNA-binding enoyl-CoA hydratase antibody; AU-binding protein/enoyl-CoA hydratase antibody; Itaconyl-CoA hydratase antibody; EC 4.2.1.56 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human AUH
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Catalyzes the conversion of 3-methylglutaconyl-CoA to 3-hydroxy-3-methylglutaryl-CoA. Also has itaconyl-CoA hydratase activity by converting itaconyl-CoA into citramalyl-CoA in the C5-dicarboxylate catabolism pathway. The C5-dicarboxylate catabolism pathway is required to detoxify itaconate, a vitamin B12-poisoning metabolite. Has very low enoyl-CoA hydratase activity. Was originally identified as RNA-binding protein that binds in vitro to clustered 5'-AUUUA-3' motifs.
  • 基因功能參考文獻：
    1. AUH localizes to the inner mitochondrial membrane and matrix where it associates with mitochondrial ribosomes and regulates protein synthesis. PMID: 24598254
    2. Phenotypic heterogeneity in two siblings with 3-methylglutaconic aciduria type I caused by a novel deletion of exons 1-3 within the AUH gene. PMID: 21840233
    3. 3-Methylglutaconic aciduria type I is caused by mutations in AUH PMID: 12434311
    4. Human 3-methylglutaconyl-CoA hydratase is identical with RNA-binding protein (AUH); molecular analyses of MGA1 patients show homozygosity or compound heterozygosity for mutations in AUH. PMID: 12655555
    5. Mutation analysis in the AUH gene revealed homozygosity for a novel splice site mutation IVS9-2A>G. We conclude that MGA1 may be associated with fever-associated seizures even in children without delayed psychomotor development. PMID: 15033206
    6. Mutations in the AUH gene are linked to metabolic disease 3-methylglutaconic aciduria type I (MGA1). PMID: 16640564
    7. The AUH trimer dimerizes upon binding to one molecule of a long RNA containing 24 repeats of the AUUU motif, (AUUU)(24)A. PMID: 18831052

    顯示更多

    收起更多

  • 相關疾病：
    3-methylglutaconic aciduria 1 (MGA1)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    Enoyl-CoA hydratase/isomerase family
  • 數據庫鏈接：

    HGNC: 890

    OMIM: 250950

    KEGG: hsa:549

    STRING: 9606.ENSP00000364883

    UniGene: Hs.175905



主站蜘蛛池模板： 免费无码黄网站在线看| 国产98在线 | 免费| 毛片无遮挡高清免费| av免费不卡国产观看| 亚洲国产一区二区波多野结衣| 无码人妻精品一区二区三| 精品乱码无人区一区二区| 亚洲中文综合网五月俺也去| 亚洲色无码中文字幕yy51999| 无码人妻精品一区二区蜜桃百度| 国产在线不卡视频免费视频| 97se亚洲精品一区二区| 国产精品99久久久久久宅男| 欧美激情一区二区三区在线| 99在线精品一区二区三区| 亚洲精品无码伊人久久| 一二三四社区在线中文视频| 亚洲一区二区三区香蕉| 人妻少妇乱子伦精品| 亚洲色无码专区在线观看| 国产精品久久久久久久免费看| 免费观看激色视频网站| 亚洲美女高清aⅴ视频免费| 正在播放国产真实露脸高清| 国产精品无码翘臀在线观看| 亚洲aⅴ无码国精品中文字慕 | 国产av仑乱内谢| 天天天天做夜夜夜夜做无码| 最新国产精品久久精品| 永久黄网站色视频免费直播| 无码一区二区三区av免费| 欧美成妇人吹潮在线播放| √最新版天堂资源网在线下载| 深夜福利在线观看视频| 无码免费午夜福利看片| 在线精品亚洲一区二区小说| 真人二十三式性视频(动)| 无码人妻精品一区二区三| 国产高清精品软件丝瓜软件| 视频分类 国内精品| 老熟女毛茸茸浓毛|