PAH
PAH,即苯丙氨酸羥化酶(Phenylalanine Hydroxylase),是一種在肝臟中表達的酶,對苯丙氨酸(Phenylalanine)的代謝起著關鍵作用。PAH具有典型的酶結構,包括催化活性中心以及與底物和輔助因子結合的位點。其催化活性中心由特定的氨基酸殘基組成,這些殘基直接參與苯丙氨酸的羥基化反應。PAH的活性受到多種因素的調控,包括基因表達、蛋白質修飾和代謝物水平等。在基因表達層面,PAH基因的表達水平受到轉錄因子的調控。在蛋白質修飾方面,PAH的活性可能受到磷酸化、糖基化等修飾的影響。此外,代謝物如苯丙氨酸和酪氨酸的水平也可能反饋調節(jié)PAH的活性。
熱銷產(chǎn)品
Recombinant Human Phenylalanine-4-hydroxylase (PAH)
驗證數(shù)據(jù)

(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.
PAH Antibodies
PAH for Homo sapiens (Human)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 種屬反應性 | 應用類型 |
---|---|---|---|
CSB-PA003698 | PAH Antibody | Human,Mouse,Rat | WB, IHC, ELISA |
CSB-PA017396LA01HU | PAH Antibody | Human, Mouse | ELISA, WB, IHC, IF |
CSB-PA017396LB01HU | PAH Antibody, HRP conjugated | Human | ELISA |
CSB-PA017396LC01HU | PAH Antibody, FITC conjugated | Human | |
CSB-PA017396LD01HU | PAH Antibody, Biotin conjugated | Human | ELISA |
CSB-RA169000A0HU | PAH Recombinant Monoclonal Antibody | Human | ELISA, IHC, IF |
PAH Proteins
PAH Proteins for Homo sapiens (Human)
產(chǎn)品貨號 | 產(chǎn)品名稱 | 來源 |
---|---|---|
CSB-BP017396HU CSB-MP017396HU CSB-EP017396HU-B |
Recombinant Human Phenylalanine-4-hydroxylase (PAH) | Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CSB-EP017396HU | Recombinant Human Phenylalanine-4-hydroxylase (PAH) | E.coli |
CSB-EP017396HUa0 | Recombinant Human Phenylalanine-4-hydroxylase (PAH) | E.coli |
CSB-EP017396HUe1 | Recombinant Human Phenylalanine-4-hydroxylase (PAH) | E.coli |
CSB-YP017396HU | Recombinant Human Phenylalanine-4-hydroxylase (PAH) | Yeast |