MMUT
MMUT(Methylmalonyl-CoA mutase)是一種對體內甲基丙二酰輔酶A(Methylmalonyl-CoA)進行轉化為琥珀酰輔酶A(Succinyl-CoA)的蛋白酶,參與人體甲基丙二酰輔酶A代謝途徑。其研究有助于理解和診斷與甲基丙二酰輔酶A代謝紊亂相關的疾病,比如甲基丙二酰輔酶A尿癥(Methylmalonic Aciduria)。(https://doi.org/10.1016/j.bbrc.2010.11.141).MMUT基因突變會導致甲基丙二酰輔酶A代謝障礙,引起先天性甲基丙二酰輔酶A尿癥(Methylmalonic Acidemia,MMA)。 研究MMUT蛋白的結構和功能可能有助于發現針對甲基丙二酰輔酶A代謝紊亂的治療方法,有助于更深入地了解代謝通路和相關遺傳病的發病機制,為未來治療方法的發展提供基礎。
熱銷產品
● Recombinant Human Endogenous retrovirus group K member 6 Env polyprotein (ERVK-6), partial
驗證數據

(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.
MMUT Antibodies
MMUT for Homo sapiens (Human)
產品貨號 | 產品名稱 | 種屬反應性 | 應用類型 |
---|---|---|---|
CSB-PA015243GA01HU | MUT Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
CSB-MA015243A0m | MMUT Monoclonal Antibody | Human, Mouse,Rat | ELISA,WB |
MMUT for Mus musculus (Mouse)
產品貨號 | 產品名稱 | 種屬反應性 | 應用類型 |
---|---|---|---|
CSB-PA015243YA01MO | Mut Antibody | Mouse | ELISA |
CSB-PA015243YB01MO | Mut Antibody, HRP conjugated | Mouse | ELISA |
CSB-PA015243YD01MO | Mut Antibody, Biotin conjugated | Mouse | ELISA |
MMUT Proteins
MMUT Proteins for Homo sapiens (Human)
產品貨號 | 產品名稱 | 來源 |
---|---|---|
CSB-YP015243HU CSB-BP015243HU CSB-MP015243HU CSB-EP015243HU-B |
Recombinant Human Methylmalonyl-CoA mutase, mitochondrial (MMUT) | Yeast Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CSB-EP015243HU | Recombinant Human Methylmalonyl-CoA mutase, mitochondrial (MMUT) | E.coli |
MMUT Proteins for Mus musculus (Mouse)
產品貨號 | 產品名稱 | 來源 |
---|---|---|
CSB-YP015243MO | Recombinant Mouse Methylmalonyl-CoA mutase, mitochondrial (Mmut) | Yeast |
CSB-EP015243MO | Recombinant Mouse Methylmalonyl-CoA mutase, mitochondrial (Mutc) | E.coli |
CSB-BP015243MO CSB-MP015243MO CSB-EP015243MO-B |
Recombinant Mouse Methylmalonyl-CoA mutase, mitochondrial (Mmut) | Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
MMUT Proteins for Sus scrofa (Pig)
產品貨號 | 產品名稱 | 來源 |
---|---|---|
CSB-YP822640PI CSB-EP822640PI CSB-BP822640PI CSB-MP822640PI CSB-EP822640PI-B |
Recombinant Pig Methylmalonyl-CoA mutase, mitochondrial (MUT), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
MMUT Proteins for Bos taurus (Bovine)
產品貨號 | 產品名稱 | 來源 |
---|---|---|
CSB-YP867072BO CSB-EP867072BO CSB-BP867072BO CSB-MP867072BO CSB-EP867072BO-B |
Recombinant Bovine Methylmalonyl-CoA mutase, mitochondrial (MUT), partial | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |