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DNM1L

DNM1L,全名為動力蛋白相關蛋白1(Drp1),是發動蛋白超家族的成員,最早在酵母中發現,故又名 DNM1。該蛋白參與線粒體和過氧化物酶體的分裂、線粒體的運輸和分布等過程,對維持線粒體正常功能至關重要。當 DNM1L 發生突變時,會導致線粒體形態異常、功能受損,進而引起能量生成不足,影響心肌細胞收縮和舒張功能,引發心肌功能障礙。研究表明,DNM1L 突變與擴張型心肌病、癲癇、腦病等多種疾病相關。目前,針對 DNM1L 相關疾病的研究主要集中在闡明其突變導致的病理機制,以及探索新的治療策略。已有研究表明,通過基因編輯技術構建遺傳背景相似的對照細胞系,可以進一步探究突變位點與疾病嚴重程度的關系,為開發針對此類疾病的新療法提供重要依據。

熱銷產品

Recombinant Human Dynamin-1-like protein (DNM1L) (CSB-EP007078HU)

驗證數據

CSB-EP007078HU

(Tris-Glycine gel) Discontinuous SDS-PAGE (reduced) with 5% enrichment gel and 15% separation gel.

CSB-EP007078HU

Based on the SEQUEST from database of E.coli host and target protein, the LC-MS/MS Analysis result of CSB-EP007078HU could indicate that this peptide derived from E.coli-expressed Homo sapiens (Human) DNM1L.

CSB-EP007078HU

Based on the SEQUEST from database of E.coli host and target protein, the LC-MS/MS Analysis result of CSB-EP007078HU could indicate that this peptide derived from E.coli-expressed Homo sapiens (Human) DNM1L.

DNM1L Antibody (CSB-PA007078EA01HU)

驗證數據

CSB-PA007078EA01HU

Western Blot
Positive WB detected in: A549 whole cell lysate, Mouse heart tissue
All lanes: DNM1L antibody at 0.5µg/ml
Secondary
Goat polyclonal to rabbit IgG at 1/50000 dilution
Predicted band size: 82, 81, 80, 79, 84, 61, 83 kDa
Observed band size: 82 kDa

CSB-PA007078EA01HU

Immunohistochemistry analysis of human cervical cancer using CSB-PA007078EA01HU at dilution of 1:100

CSB-PA007078EA01HU

Immunohistochemistry analysis of human brain tissue using CSB-PA007078EA01HU at dilution of 1:100

DNM1L Antibodies

DNM1L for Homo sapiens (Human)

DNM1L Proteins

DNM1L Proteins for Homo sapiens (Human)

DNM1L Proteins for Rattus norvegicus (Rat)

DNM1L Proteins for Bos taurus (Bovine)

DNM1L Proteins for Danio rerio (Zebrafish) (Brachydanio rerio)

DNM1L Proteins for Mus musculus (Mouse)



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