在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. NDUFA1 Antibody

NDUFA1 Antibody

  • 中文名稱：
    NDUFA1兔多克隆抗體
  • 貨號：
    CSB-PA271484
  • 規格：
    ￥1100
  • 圖片：
    • The image on the left is immunohistochemistry of paraffin-embedded Human colon cancer tissue using CSB-PA271484(NDUFA1 Antibody) at dilution 1/30, on the right is treated with fusion protein. (Original magnification: ×200)
    • The image on the left is immunohistochemistry of paraffin-embedded Human brain tissue using CSB-PA271484(NDUFA1 Antibody) at dilution 1/30, on the right is treated with fusion protein. (Original magnification: ×200)
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
  • 別名：
    NDUFA1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1; Complex I-MWFE; CI-MWFE; NADH-ubiquinone oxidoreductase MWFE subunit
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Fusion protein of Human NDUFA1
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    Non-conjugated
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen affinity purification
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    -20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,IHC
  • 推薦稀釋比：
    Application Recommended Dilution
    ELISA 1:2000-1:5000
    IHC 1:50-1:200
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone.
  • 基因功能參考文獻：
    1. Results from a study on gene expression variability markers in early-stage human embryos shows that NDUF1A is a putative expression variability marker for the 3-day, 8-cell embryo stage. PMID: 26288249
    2. The gene signature of OPA1, CTSA, NDUFA1, STK10 and PRDX1 was able to identify patients post-implant with a sensitivity of 91% and a specificity of 86% in discrimination between post-implant group and healthy controls. PMID: 27177495
    3. Fanconi anemia complementation group A mutants show defective respiration through Complex I, diminished ATP production and metabolic sufferance with an increased AMP/ATP ratio. PMID: 23791750
    4. Heterozygous mutation in the X chromosomal NDUFA1 gene in a girl with complex I deficiency PMID: 21596602
    5. Mutations in the NDUFA1 gene is linked to a delayed mitochondrial network recovery in OXPHOS disorders. PMID: 20153825
    6. Species-specific and mutant MWFE proteins effect on the assembly of a functional mammalian mitochondrial complex I. PMID: 11937507
    7. A family-based association study finds that the NDUFA1 gene is unlikely to harbor a major visual loss susceptibility locus for Leber hereditary optic neuropathy. PMID: 12084895
    8. Oxidative stress and partial deficiencies of mitochondrial complex I are key factors in the pathogenesis of Parkinson's disease. (REVIEW) PMID: 15038604
    9. Suppression of NDUFA1 expression could represent a key pathogenic mechanism in the development of basal cell carcinoma PMID: 15854127
    10. Two novel p.Gly8Arg and p.Arg37Ser hemizygous mutations in NDUFA1 were identified in two unrelated male patients presenting with Leigh's syndrome and with myoclonic epilepsy and developmental delay. PMID: 17262856
    11. hypothesize that the novel G32R mutation in NDUFA1 is causing complex I deficiency either by itself or in synergy with additional mtDNA variants PMID: 19185523

    顯示更多

    收起更多

  • 相關疾病：
    Mitochondrial complex I deficiency (MT-C1D)
  • 亞細胞定位：
    Mitochondrion inner membrane; Single-pass membrane protein; Matrix side.
  • 蛋白家族：
    Complex I NDUFA1 subunit family
  • 組織特異性：
    Primarily expressed in heart and skeletal muscle.
  • 數據庫鏈接：

    HGNC: 7683

    OMIM: 252010

    KEGG: hsa:4694

    STRING: 9606.ENSP00000360492

    UniGene: Hs.534168



主站蜘蛛池模板： 好湿好紧太硬了我太爽了视频| 大又大又粗又硬又爽少妇毛片| 少妇激情一区二区三区视频小说| 无码专区aaaaaa免费视频| 18禁亚洲深夜福利人口| 久久久久99精品成人品| 国产在线精品99一区不卡| 爽爽影院免费观看视频| 9九色桋品熟女内射| 中文字幕漂亮人妻熟睡中被公侵犯 | 国产熟妇另类久久久久久| 久久精品超碰av无码| 国产精品99无码一区二区| 亚洲人成人无码网www国产 | 亚洲日韩av无码一区二区三区人| 久久国内精品自在自线观看| 人妻熟女一区二区aⅴ清水理纱| 少妇高潮灌满白浆毛片免费看 | 亚洲精品综合欧美一区二区三区| 自拍偷自拍亚洲精品情侣| 亚洲乱码精品久久久久..| 国产成人卡2卡3卡4乱码| 成人免费精品网站在线观看影片| 欧洲精品久久久av无码电影| 色五月丁香五月综合五月4438| av免费播放一区二区三区| 亚洲色www成人永久网址| 国产乱人伦app精品久久| 亚洲欧美色αv在线影视| 国产放荡对白视频在线观看| √天堂中文官网8在线| 国产精品久久久久无码av色戒| 狠狠躁日日躁夜夜躁2022麻豆| 国产在线码观看超清无码视频| 欧美人与动牲交免费观看| 四虎精品成人免费视频| 亚洲午夜久久久久妓女影院| 日韩精品无码去免费专区| 绝顶高潮合集videos| _97夜夜澡人人爽人人喊_欧美| 97无码免费人妻超级碰碰碰碰|