在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial (ACADSB)

  • 中文名稱:
    Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial(ACADSB)
  • 貨號:
    CSB-YP001128HU
  • 規格:
  • 來源:
    Yeast
  • 其他:
  • 中文名稱:
    Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial(ACADSB)
  • 貨號:
    CSB-EP001128HU
  • 規格:
  • 來源:
    E.coli
  • 其他:
  • 中文名稱:
    Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial(ACADSB)
  • 貨號:
    CSB-EP001128HU-B
  • 規格:
  • 來源:
    E.coli
  • 共軛:
    Avi-tag Biotinylated

    E. coli biotin ligase (BirA) is highly specific in covalently attaching biotin to the 15 amino acid AviTag peptide. This recombinant protein was biotinylated in vivo by AviTag-BirA technology, which method is BriA catalyzes amide linkage between the biotin and the specific lysine of the AviTag.

  • 其他:
  • 中文名稱:
    Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial(ACADSB)
  • 貨號:
    CSB-BP001128HU
  • 規格:
  • 來源:
    Baculovirus
  • 其他:
  • 中文名稱:
    Recombinant Human Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial(ACADSB)
  • 貨號:
    CSB-MP001128HU
  • 規格:
  • 來源:
    Mammalian cell
  • 其他:

產品詳情

  • 純度:
    >85% (SDS-PAGE)
  • 基因名:
    ACADSB
  • Uniprot No.:
  • 別名:
    2 MEBCAD; 2 methyl branched chain acyl CoA dehydrogenase; 2 methylbutyryl CoA dehydrogenase; 2 methylbutyryl coenzyme A dehydrogenase; 2-MEBCAD; 2-methyl branched chain acyl-CoA dehydrogenase; 2-methylbutyryl-CoA dehydrogenase; 2-methylbutyryl-coenzyme A dehydrogenase; ACAD7; ACADSB; ACDSB_HUMAN; acyl CoA dehydrogenase; short/branched chain; acyl Coenzyme A dehydrogenase short branched chain; mitochondrial; OTTHUMP00000020685; OTTHUMP00000046795; SBCAD; Short/branched chain specific acyl-CoA dehydrogenase; short/branched chain specific acyl-CoA dehydrogenase; mitochondrial
  • 種屬:
    Homo sapiens (Human)
  • 蛋白長度:
    Full Length of Mature Protein
  • 表達區域:
    34-432
  • 氨基酸序列
    KSSQSEA LLNITNNGIH FAPLQTFTDE EMMIKSSVKK FAQEQIAPLV STMDENSKME KSVIQGLFQQ GLMGIEVDPE YGGTGASFLS TVLVIEELAK VDASVAVFCE IQNTLINTLI RKHGTEEQKA TYLPQLTTEK VGSFCLSEAG AGSDSFALKT RADKEGDYYV LNGSKMWISS AEHAGLFLVM ANVDPTIGYK GITSFLVDRD TPGLHIGKPE NKLGLRASST CPLTFENVKV PEANILGQIG HGYKYAIGSL NEGRIGIAAQ MLGLAQGCFD YTIPYIKERI QFGKRLFDFQ GLQHQVAHVA TQLEAARLLT YNAARLLEAG KPFIKEASMA KYYASEIAGQ TTSKCIEWMG GVGYTKDYPV EKYFRDAKIG TIYEGASNIQ LNTIAKHIDA EY
  • 蛋白標簽:
    Tag?type?will?be?determined?during?the?manufacturing?process.
    The tag type will be determined during production process. If you have specified tag type, please tell us and we will develop the specified tag preferentially.
  • 產品提供形式:
    Lyophilized powder
    Note: We will preferentially ship the format that we have in stock, however, if you have any special requirement for the format, please remark your requirement when placing the order, we will prepare according to your demand.
  • 復溶:
    We recommend that this vial be briefly centrifuged prior to opening to bring the contents to the bottom. Please reconstitute protein in deionized sterile water to a concentration of 0.1-1.0 mg/mL.We recommend to add 5-50% of glycerol (final concentration) and aliquot for long-term storage at -20℃/-80℃. Our default final concentration of glycerol is 50%. Customers could use it as reference.
  • 儲存條件:
    Store at -20°C/-80°C upon receipt, aliquoting is necessary for mutiple use. Avoid repeated freeze-thaw cycles.
  • 保質期:
    The shelf life is related to many factors, storage state, buffer ingredients, storage temperature and the stability of the protein itself.
    Generally, the shelf life of liquid form is 6 months at -20°C/-80°C. The shelf life of lyophilized form is 12 months at -20°C/-80°C.
  • 貨期:
    Delivery time may differ from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
    Note: All of our proteins are default shipped with normal blue ice packs, if you request to ship with dry ice, please communicate with us in advance and extra fees will be charged.
  • 注意事項:
    Repeated freezing and thawing is not recommended. Store working aliquots at 4°C for up to one week.
  • Datasheet :
    Please contact us to get it.

產品評價

靶點詳情

  • 功能:
    Short and branched chain specific acyl-CoA dehydrogenase that catalyzes the removal of one hydrogen from C-2 and C-3 of the fatty acyl-CoA thioester, resulting in the formation of trans-2-enoyl-CoA. Among the different mitochondrial acyl-CoA dehydrogenases, acts specifically on short and branched chain acyl-CoA derivatives such as (S)-2-methylbutyryl-CoA as well as short straight chain acyl-CoAs such as butyryl-CoA. Plays an important role in the metabolism of L-isoleucine by catalyzing the dehydrogenation of 2-methylbutyryl-CoA, one of the steps of the L-isoleucine catabolic pathway. Can also act on valproyl-CoA, a metabolite of valproic acid, an antiepileptic drug.
  • 基因功能參考文獻:
    1. the c.1165 A>G mutation before knowing whether the optimal screening cut-off would minimize true positives or false negatives for SBCADD associated with this mutation. PMID: 23712021
    2. Strong candidate gene for mitochondrial disease, based on recessive mutations detected in infantile patients PMID: 22277967
    3. These findings confirm that SBCAD deficiency can be identified through newborn screening by acylcarnitine analysis. PMID: 20547083
    4. Differences between the rat and human enzyme at positions 383, 222, and 220 alter substrate specificity without affecting substrate binding. PMID: 12855692
    5. Identification and characterization of an IVS3+3A>G mutation (c.303+3A>G) in the SBCAD gene, and provide evidence that this mutation is disease-causing. PMID: 16317551
    6. Results examine the mechanistic basis for dysfunction of the common variant short-chain acyl-CoA dehydrogenases and demonstrate that mutations can have a large impact on the redox properties of the enzyme. PMID: 16331963
    7. Results indicate that substrate redox activation occurs in short-chain acyl-CoA dehydrogenase leading to a large enzyme midpoint potential shift. PMID: 16331964

    顯示更多

    收起更多

  • 相關疾病:
    Short/branched-chain acyl-CoA dehydrogenase deficiency (SBCADD)
  • 亞細胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Acyl-CoA dehydrogenase family
  • 組織特異性:
    Ubiquitously expressed.
  • 數據庫鏈接:

    HGNC: 91

    OMIM: 600301

    KEGG: hsa:36

    STRING: 9606.ENSP00000357873

    UniGene: Hs.81934



主站蜘蛛池模板: 亚洲国产午夜精华无码福利| 性色av无码久久一区二区三区| 久久久久久久97| 超碰97人人射妻| 天天狠天天天天透在线| 亚洲成在人线av品善网好看| 3d成人h动漫网站入口| 国产精品白浆无码流出视频| 全免费又大粗又黄又爽少妇片| 国产精品日本一区二区在线播放| 狠狠亚洲婷婷综合色香五月排名| 亚洲日韩日本中文在线| 久久97超碰色中文字幕蜜芽| 日本一卡2卡3卡4卡无卡免费网站 丰满少妇人妻无码专区 | 国产成人国拍亚洲精品| 国产精品天干在线观看| 亚洲中文字幕无码久久| 亚洲天堂男人影院| 长腿校花无力呻吟娇喘| 女人高潮抽搐潮喷小视频| 精品无码专区亚洲| 一区二区视频| 色婷婷综合久久久久中文一区二区 | 国产高清av在线播放| 日韩精品无码免费一区二区三区| 亚洲精品午夜无码电影网| 性饥渴少妇av无码毛片| 免费的黄网站在线观看| 亚洲人成无码区在线观看| 尹人香蕉99久久综合网站| 无码人妻一区二区三区av| 10000部拍拍拍免费视频| 国产ae86亚洲福利入口| 日本www网站色情乱码| 亚洲 小说 欧美 激情 另类| 肉大榛一进一出免费视频| 成人亚洲欧美日韩在线观看| 国内午夜熟妇又乱又伦| 欧美成人一区二区三区片免费| 伊人久久大香线蕉亚洲| 亚洲国产精品久久久久爰|