在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. WBSCR16 Antibody

WBSCR16 Antibody

  • 中文名稱：
    WBSCR16兔多克隆抗體
  • 貨號：
    CSB-PA025981GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    RCC1L
  • 別名：
    5730496C04Rik antibody; AU019812 antibody; DKFZp434D0421 antibody; MGC189739 antibody; MGC44931 antibody; RCC1-like G exchanging factor-like protein antibody; WBS16_HUMAN antibody; Wbscr16 antibody; Williams-Beuren syndrome chromosomal region 16 protein antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human WBSCR16
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Guanine nucleotide exchange factor (GEF) for mitochondrial dynamin-related GTPase OPA1. Activates OPA1, by exchanging bound GDP for free GTP, and drives OPA1 and MFN1-dependent mitochondrial fusion. Plays an essential role in mitochondrial ribosome biogenesis. As a component of a functional protein-RNA module, consisting of RCC1L, NGRN, RPUSD3, RPUSD4, TRUB2, FASTKD2 and 16S mitochondrial ribosomal RNA (16S mt-rRNA), controls 16S mt-rRNA abundance and is required for intra-mitochondrial translation of core subunits of the oxidative phosphorylation system.
  • 基因功能參考文獻：
    1. Using X-ray crystallography, established the structure of human Williams-Beuren Syndrome Chromosomal Region 16 (WBSCR16), and showed that WBSCR16 has seven-bladed b-propeller fold (the RCC1 fold) with unique surface features. PMID: 28608466
  • 相關疾病：
    WBSCR16 is located in the Williams-Beuren syndrome (WBS) critical region. WBS results from a hemizygous deletion of several genes on chromosome 7q11.23, thought to arise as a consequence of unequal crossing over between highly homologous low-copy repeat sequences flanking the deleted region. Haploinsufficiency of WBSCR16 may be the cause of certain cardiovascular and musculo-skeletal abnormalities observed in the disease.
  • 亞細胞定位：
    Mitochondrion membrane. Mitochondrion inner membrane.
  • 組織特異性：
    Ubiquitous.
  • 數據庫鏈接：

    HGNC: 14948

    OMIM: 194050

    KEGG: hsa:81554

    STRING: 9606.ENSP00000333799

    UniGene: Hs.529623



主站蜘蛛池模板： 国产精品特黄aaaa片在线观看| 一本无码中文字幕在线观| 亚洲综合天堂一区二区三区| 激情航班h版在线观看| 亚洲全部无码中文字幕| 四虎av永久在线精品免费观看| 肥老熟妇伦子伦456视频| 爆爽久久久一区二区又大又黄又嫩 | 在线看免费无码av天堂的| gv天堂gv无码男同在线观看| 最近更新中文字幕| av在线亚洲男人的天堂| 99久久无色码中文字幕人妻蜜柚| 丁香五月激情综合亚洲| 亚洲精品久久久av无码专区| 女女女女女裸体处开bbb| 精品少妇人妻av一区二区三区| 在线看片免费人成视频福利| 亚洲高请码在线精品av| 99久久精品6在线播放| 少妇高潮毛片免费看| 色老久久精品偷偷鲁| 亚洲中文字幕码在线电影| h人成在线看免费视频| 亚洲国产精久久久久久久| 揄拍成人国产精品视频| 日韩精品av一区二区三区| 亚洲国产精品无码7777一线| 欧美3p两根一起进高清视频| 人妻少妇无码精品视频区| 国产精品国产三级国产aⅴ下载| 色一情一乱一伦一区二区三区小说| 国产精品久人妻精品老妇 | 精品露脸国产偷人在视频| 影音先锋男人av鲁色资源网| 亚洲成a人片在线观看中文| 国产日产欧产精品精品推荐免费| 国产一区丝袜高跟鞋| 真人无码作爱免费视频| 日本护士毛茸茸高潮| 中文字日产乱码免费1～3软件 |