在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

WBSCR16 Antibody

  • 中文名稱:
    WBSCR16兔多克隆抗體
  • 貨號:
    CSB-PA025981GA01HU
  • 規格:
    ¥3,900
  • 其他:

產品詳情

  • Uniprot No.:
  • 基因名:
    RCC1L
  • 別名:
    5730496C04Rik antibody; AU019812 antibody; DKFZp434D0421 antibody; MGC189739 antibody; MGC44931 antibody; RCC1-like G exchanging factor-like protein antibody; WBS16_HUMAN antibody; Wbscr16 antibody; Williams-Beuren syndrome chromosomal region 16 protein antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse,Rat
  • 免疫原:
    Human WBSCR16
  • 免疫原種屬:
    Homo sapiens (Human)
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen Affinity Purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB,IHC
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Guanine nucleotide exchange factor (GEF) for mitochondrial dynamin-related GTPase OPA1. Activates OPA1, by exchanging bound GDP for free GTP, and drives OPA1 and MFN1-dependent mitochondrial fusion. Plays an essential role in mitochondrial ribosome biogenesis. As a component of a functional protein-RNA module, consisting of RCC1L, NGRN, RPUSD3, RPUSD4, TRUB2, FASTKD2 and 16S mitochondrial ribosomal RNA (16S mt-rRNA), controls 16S mt-rRNA abundance and is required for intra-mitochondrial translation of core subunits of the oxidative phosphorylation system.
  • 基因功能參考文獻:
    1. Using X-ray crystallography, established the structure of human Williams-Beuren Syndrome Chromosomal Region 16 (WBSCR16), and showed that WBSCR16 has seven-bladed b-propeller fold (the RCC1 fold) with unique surface features. PMID: 28608466
  • 相關疾病:
    WBSCR16 is located in the Williams-Beuren syndrome (WBS) critical region. WBS results from a hemizygous deletion of several genes on chromosome 7q11.23, thought to arise as a consequence of unequal crossing over between highly homologous low-copy repeat sequences flanking the deleted region. Haploinsufficiency of WBSCR16 may be the cause of certain cardiovascular and musculo-skeletal abnormalities observed in the disease.
  • 亞細胞定位:
    Mitochondrion membrane. Mitochondrion inner membrane.
  • 組織特異性:
    Ubiquitous.
  • 數據庫鏈接:

    HGNC: 14948

    OMIM: 194050

    KEGG: hsa:81554

    STRING: 9606.ENSP00000333799

    UniGene: Hs.529623



主站蜘蛛池模板: 国产成人精品日本亚洲18| 顶级欧美熟妇xx| 性色av极品无码专区亚洲| 成人精品一区二区三区中文字幕| 日韩国产亚洲欧美中国v| 亚洲国产制服丝袜先锋| 久久亚洲国产成人精品性色| 90后极品粉嫩小泬20p| 国产精品亚洲精品日韩已满| 人妻少妇偷人无码视频| 伊人色合天天久久综合网| 一品二品三品中文字幕| 国内偷自第一区二区三区| 亚洲欧美人高清精品a∨| 中国熟妇人妻xxxxx| 亚洲第一区无码专区| 国产乱码免费卡1卡二卡3| 欧美日本日韩aⅴ在线视频| 亚洲丁香婷婷久久一区二区| 欧美xxxx做受欧美| 大香线蕉伊人超碰| 国产精品欧美成人| 国产在线无码一区二区三区视频 | 久久国产精品-国产精品| 亚洲综合一区二区三区四区五区| 黑人与人妻无码中字视频| 国产a∨精品一区二区三区不卡| 永久免费无码日韩视频| 精品国产一区二区三区久久狼| 成人三级视频在线观看一区二区| 中文字幕人妻无码视频| 免费特级黄毛片| 插插无码视频大全不卡网站| 亚洲日韩性欧美中文字幕| 亚洲成av人片在线观看橙子| 小泽玛利亚一区二区在线观看| 92久久精品一区二区| 亚洲性夜夜综合久久7777| 久久久97丨国产人妻熟女| 中文字幕日韩一区二区三区不卡| 国产乱码免费卡1卡二卡3|