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TSR2 Antibody, FITC conjugated

  • 中文名稱:
    TSR2兔多克隆抗體, FITC偶聯
  • 貨號:
    CSB-PA836166HC01HU
  • 規格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) TSR2 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    TSR2
  • 別名:
    DT1P1A10 antibody; Pre-rRNA-processing protein TSR2 homolog antibody; RP1 112K5 2 antibody; TSR2 20S rRNA accumulation homolog antibody; TSR2 20S rRNA accumulation homolog S cerevisiae antibody; tsr2 antibody; TSR2_HUMAN antibody; WGG motif containing 1 antibody; WGG1 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Pre-rRNA-processing protein TSR2 homolog protein (1-191AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式:
    Liquid
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    May be involved in 20S pre-rRNA processing.
  • 基因功能參考文獻:
    1. A likely pathogenic X-linked mutation affecting a highly conserved residue was found in TSR2 and De novo mutations affecting the RPS28 start codon were found in two unrelated probands, identifying RPS28 as a novel disease gene. PMID: 24942156
    2. This data for the first time suggests that TSR2 is involved in the NF-kappaB signaling pathway and may regulate apoptosis. PMID: 21790011
  • 相關疾病:
    Diamond-Blackfan anemia 14, with mandibulofacial dysostosis (DBA14)
  • 蛋白家族:
    TSR2 family
  • 數據庫鏈接:

    HGNC: 25455

    OMIM: 300945

    KEGG: hsa:90121

    STRING: 9606.ENSP00000364293

    UniGene: Hs.522662



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