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TMEM87B Antibody, HRP conjugated

  • 中文名稱:
    TMEM87B兔多克隆抗體, HRP偶聯(lián)
  • 貨號:
    CSB-PA023891LB01HU
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) TMEM87B Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    TMEM87B
  • 別名:
    TMEM87B; Transmembrane protein 87B
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Transmembrane protein 87B protein (451-554AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    HRP
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評價

靶點詳情

  • 功能:
    May be involved in retrograde transport from endosomes to the trans-Golgi network (TGN).
  • 基因功能參考文獻:
    1. Heterozygous loss of FBLN7 and TMEM87B account for some of the clinical features, including cardiac defects and craniofacial abnormalities associated with 2q13 deletion syndrome. PMID: 24694933
  • 相關(guān)疾病:
    TMEM87B mutations may be involved in restrictive cardiomyopathy (RCM), a rare non-ischemic myocardial disease. RCM is characterized by restrictive ventricular-filling physiology in the presence of normal or reduced diastolic and/or systolic volumes (of 1 or both ventricles), biatrial enlargement, and normal ventricular wall thickness.
  • 亞細胞定位:
    Golgi apparatus membrane; Multi-pass membrane protein.
  • 蛋白家族:
    LU7TM family, TMEM87 subfamily
  • 數(shù)據(jù)庫鏈接:

    HGNC: 25913

    OMIM: 617203

    KEGG: hsa:84910

    STRING: 9606.ENSP00000283206

    UniGene: Hs.656298



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