在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. POMK Antibody, FITC conjugated

POMK Antibody, FITC conjugated

  • 中文名稱：
    POMK兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA863985LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) POMK Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    POMK
  • 別名：
    FLJ23356 antibody; MDDGA12 antibody; POMK antibody; Probable inactive protein kinase-like protein SgK196 antibody; Protein kinase like protein SgK196 antibody; Protein kinase-like protein SgK196 antibody; Protein O-mannose kinase antibody; SG196_HUMAN antibody; SGK196 antibody; Sugen kinase 196 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Protein O-mannose kinase protein (44-350AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Protein O-mannose kinase that specifically mediates phosphorylation at the 6-position of an O-mannose of the trisaccharide (N-acetylgalactosamine (GalNAc)-beta-1,3-N-acetylglucosamine (GlcNAc)-beta-1,4-mannose) to generate phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-1,3-N-acetylglucosamine-beta-1,4-(phosphate-6-)mannose). Phosphorylated O-mannosyl trisaccharide is a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity. Only shows kinase activity when the GalNAc-beta-3-GlcNAc-beta-terminus is linked to the 4-position of O-mannose, suggesting that this disaccharide serves as the substrate recognition motif.
  • 基因功能參考文獻：
    1. POMK mutations disrupt muscle development leading to a spectrum of neuromuscular presentations. PMID: 24925318
    2. Homozygous truncating mutations in POMK lead to congenital muscular dystrophies with secondary merosin deficiency, hypomyelination and intellectual disability. PMID: 24556084
    3. These findings suggest how mutations in GTDC2, B3GALNT2, and SGK196 disrupt dystroglycan receptor function and lead to congenital muscular dystrophy. PMID: 23929950
  • 相關疾病：
    Muscular dystrophy-dystroglycanopathy congenital with brain and eye anomalies A12 (MDDGA12); Muscular dystrophy-dystroglycanopathy limb-girdle C12 (MDDGC12)
  • 亞細胞定位：
    Endoplasmic reticulum membrane; Single-pass type II membrane protein.
  • 蛋白家族：
    Protein kinase superfamily, Ser/Thr protein kinase family, STKL subfamily
  • 組織特異性：
    Highest expression is observed in brain, skeletal muscle, kidney and heart in fetal and adult tissues.
  • 數據庫鏈接：

    HGNC: 26267

    OMIM: 615247

    KEGG: hsa:84197

    STRING: 9606.ENSP00000331258

    UniGene: Hs.491646



主站蜘蛛池模板： 久久国产亚洲精品无码| 国产午夜aaaaa片在线影院| 九色精品国产成人综合网站| 日韩一区二区三免费高清| 国产精品原创av片国产日韩| 日产中文字幕在线观看| 天天爽夜夜爽夜夜爽| 女人扒下裤让男人桶到爽| 无码av专区丝袜专区| 欧洲精品码一区二区三区免费看 | wwww亚洲熟妇久久久久| 人人妻人人藻人人爽欧美一区| 国产成人精品日本亚洲一区| 永久免费精品成人网站| 国产精品二区一区二区aⅴ污介绍| 欧美性猛交xxxx免费看蜜桃| 国产精品v欧美精品∨日韩| 国产麻豆精品av在线观看| 女狠狠噜天天噜日日噜| 国产精品成人午夜久久| 国产午夜福利短视频| 色一情一乱一伦一区二区三区| 欧美性xxxx极品hd欧美风情| 丰满白嫩人妻中出无码| 亚洲精品一区二区久久| 国产三区在线成人av| 无码中出人妻中文字幕av| 上海少妇高潮狂叫喷水了| 影音先锋无码aⅴ男人资源站| 日本免费人成视频播放| 中国人妻被两个老外三p| 日韩一区二区三区四区区区| 久久丫精品忘忧草西安产品| 国产suv精品一区二人妻| 成人做受视频试看120秒| 东北妇女xx做爰视频| 荫蒂被男人添的好舒服爽免费视频 | 久久精品国产大片免费观看| 亚洲狠狠色丁香婷婷综合| 日韩~欧美一中文字幕| 午夜片无码区私人影院|