在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. POMK Antibody, FITC conjugated

POMK Antibody, FITC conjugated

  • 中文名稱：
    POMK兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA863985LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) POMK Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    POMK
  • 別名：
    FLJ23356 antibody; MDDGA12 antibody; POMK antibody; Probable inactive protein kinase-like protein SgK196 antibody; Protein kinase like protein SgK196 antibody; Protein kinase-like protein SgK196 antibody; Protein O-mannose kinase antibody; SG196_HUMAN antibody; SGK196 antibody; Sugen kinase 196 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Protein O-mannose kinase protein (44-350AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Protein O-mannose kinase that specifically mediates phosphorylation at the 6-position of an O-mannose of the trisaccharide (N-acetylgalactosamine (GalNAc)-beta-1,3-N-acetylglucosamine (GlcNAc)-beta-1,4-mannose) to generate phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-1,3-N-acetylglucosamine-beta-1,4-(phosphate-6-)mannose). Phosphorylated O-mannosyl trisaccharide is a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity. Only shows kinase activity when the GalNAc-beta-3-GlcNAc-beta-terminus is linked to the 4-position of O-mannose, suggesting that this disaccharide serves as the substrate recognition motif.
  • 基因功能參考文獻：
    1. POMK mutations disrupt muscle development leading to a spectrum of neuromuscular presentations. PMID: 24925318
    2. Homozygous truncating mutations in POMK lead to congenital muscular dystrophies with secondary merosin deficiency, hypomyelination and intellectual disability. PMID: 24556084
    3. These findings suggest how mutations in GTDC2, B3GALNT2, and SGK196 disrupt dystroglycan receptor function and lead to congenital muscular dystrophy. PMID: 23929950
  • 相關疾病：
    Muscular dystrophy-dystroglycanopathy congenital with brain and eye anomalies A12 (MDDGA12); Muscular dystrophy-dystroglycanopathy limb-girdle C12 (MDDGC12)
  • 亞細胞定位：
    Endoplasmic reticulum membrane; Single-pass type II membrane protein.
  • 蛋白家族：
    Protein kinase superfamily, Ser/Thr protein kinase family, STKL subfamily
  • 組織特異性：
    Highest expression is observed in brain, skeletal muscle, kidney and heart in fetal and adult tissues.
  • 數據庫鏈接：

    HGNC: 26267

    OMIM: 615247

    KEGG: hsa:84197

    STRING: 9606.ENSP00000331258

    UniGene: Hs.491646



主站蜘蛛池模板： 国产亚洲产品影视在线产品| 人妻丰满av无码久久不卡| 日本55丰满熟妇厨房伦| 在线亚洲高清揄拍自拍一品区| 中文成人无码精品久久久动漫| 巨乳美乳一区二区三区| 亚洲乱码国产乱码精品精| 性欧美暴力猛交69hd| 亚洲国产精品成人天堂| 国产精品 自在自线| 女人被狂躁高潮啊的视频在线看| 精品人妻系列无码一区二区三区| 波多野结衣av无码| 亚洲女人自熨在线视频| 国产三级农村妇女在线 | 午夜免费国产体验区免费的| 丁香狠狠色婷婷久久综合| 2019日韩中文字幕mv| 亚洲妓女综合网99| 亚洲 欧美 日韩 综合aⅴ电影| 人人妻人人超人人| 久久久久国产a免费观看rela| 亚洲精品一区二区三区婷婷月| 天干天干夜啦天干天干国产| 国产亚洲精品自在久久vr| 热99re久久精品| 国产96在线 | 欧美| 新版资源天堂中文| 亚洲精品少妇高清30p| 亚洲欧美在线观看| 无码中文字幕色专区| 国产白丝精品爽爽久久蜜臀| www一区二区乱码www| 国产欧美va天堂在线观看视频下载 | 天堂а在线中文在线新版| 人妻大战黑人白浆狂泄| 精品亚洲一区二区三区在线播放 | 亚洲精品无码专区在线播放| 无码人妻丰满熟妇啪啪欧美| 国产精品一区二区在线观看| 久久婷婷丁香七月色综合|