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PIH1D3 Antibody, FITC conjugated

  • 中文名稱:
    PIH1D3兔多克隆抗體, FITC偶聯(lián)
  • 貨號(hào):
    CSB-PA878855LC01HU
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) PIH1D3 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    PIH1D3
  • 別名:
    PIH1D3 antibody; CXorf41 antibody; Protein PIH1D3 antibody; PIH1 domain-containing protein 3 antibody; Sarcoma antigen NY-SAR-97 antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human
  • 免疫原:
    Recombinant Human Protein PIH1D3 protein (1-214AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標(biāo)記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能:
    Plays a role in cytoplasmic pre-assembly of axonemal dynein.
  • 基因功能參考文獻(xiàn):
    1. Study propose that PIH1D3 is part of a complementary conserved R2TP-like HSP90 co-chaperone complex, the loss of which affects assembly of a subset of inner arm dyneins. PMID: 28176794
    2. Mutations in PIH1D3 Cause X-Linked Primary Ciliary Dyskinesia with Outer and Inner Dynein Arm Defects PMID: 28041644
  • 相關(guān)疾病:
    Ciliary dyskinesia, primary, 36, X-linked (CILD36)
  • 亞細(xì)胞定位:
    Cytoplasm. Golgi apparatus, trans-Golgi network.
  • 蛋白家族:
    PIH1 family
  • 組織特異性:
    Expressed in testis, small intestine, prostate, adrenal gland, spleen, lung, bladder, breast and ovary. Expressed in ciliated epithelial cells.
  • 數(shù)據(jù)庫鏈接:

    HGNC: 28570

    OMIM: 300933

    KEGG: hsa:139212

    STRING: 9606.ENSP00000337757

    UniGene: Hs.128836



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