在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. PIGV Antibody, FITC conjugated

PIGV Antibody, FITC conjugated

  • 中文名稱：
    PIGV兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA868321LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) PIGV Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    PIGV
  • 別名：
    GPI mannosyltransferase 2 antibody; GPI mannosyltransferase II antibody; GPI MT II antibody; GPI-MT-II antibody; Phosphatidylinositol glycan biosynthesis class V protein antibody; Phosphatidylinositol-glycan biosynthesis class V protein antibody; PIG-V antibody; Pigv antibody; PIGV_HUMAN antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human GPI mannosyltransferase 2 protein (400-469AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Alpha-1,6-mannosyltransferase involved in glycosylphosphatidylinositol-anchor biosynthesis. Transfers the second mannose to the glycosylphosphatidylinositol during GPI precursor assembly.
  • 基因功能參考文獻：
    1. Data indicate that mannosyltransferases PIGV mutations are the major cause of hyperphosphatasia-mental retardation syndrome (HPMRS) which displays a broad clinical variability regarding associated malformations and growth patterns. PMID: 24129430
    2. PIGV is the rate-limiting enzyme in GPI biosynthesis under limited dolicholphosphate mannose availability. PMID: 23694781
    3. Hyperphosphatasia resulted from secretion of ALP, a GPI-anchored protein normally expressed on the cell surface, into serum due to PIGV deficiency. PMID: 22228761
    4. novel compound heterozygous mutations in the PIGV gene c.467G>A and c.1022C>A and a homozygous mutation c.1022C>A in hyperphosphatasia-mental retardation syndrome PMID: 21739589
    5. PIGV mutations are associated with hyperphosphatasia mental retardation syndrome. PMID: 20802478
    6. PIG-V is the second mannosyltransferase in GPI anchor biosynthesis. PMID: 15623507

    顯示更多

    收起更多

  • 相關疾?。?/div>
    Hyperphosphatasia with mental retardation syndrome 1 (HPMRS1)
  • 亞細胞定位：
    Endoplasmic reticulum membrane; Multi-pass membrane protein.
  • 蛋白家族：
    PIGV family
  • 數據庫鏈接：

    HGNC: 26031

    OMIM: 239300

    KEGG: hsa:55650

    STRING: 9606.ENSP00000078527

    UniGene: Hs.259605



主站蜘蛛池模板： 久久这里有精品国产电影网| 欧美熟妇性开放| 亚洲精品欧美精品日韩精品| 欧美精品1卡二卡三卡四卡| 少妇人妻无码专区在线视频| 精品国偷自产在线| 亚洲乱码国产乱码精品精大量| 超级碰97直线国产免费公开| 中文字幕韩国三级理论| 韩国日本三级在线观看| 亚洲∧v久久久无码精品| 色avav色av爱avav亚洲色拍| 国产精品久久久久无码av1| 黑人巨大精品欧美| 国产人妻aⅴ色偷| 性国产牲交xxxxx视频| 热久久视久久精品18| 强睡邻居人妻中文字幕| 国产成人精品日本亚洲18| 男女猛烈无遮挡免费视频app | 欧洲熟妇色xxxx欧美老妇多毛| 美女啪啪网站又黄又免费| 亚洲熟妇av午夜无码不卡| 在线亚洲97se亚洲综合在线| 欧美老熟妇欲乱高清视频| 少妇内射兰兰久久| 狠狠色噜噜狠狠狠狠米奇777| 无码乱人伦一区二区亚洲| 熟女少妇内射日韩亚洲| 国产毛片不卡野外视频| 欧美在线观看免费专区| 乱女伦露脸对白在线播放| 人妻精品久久久久中文字幕| 一本色道久久综合狠狠躁篇| 中文天堂网www新版资源在线| 国产肥熟女视频一区二区三区| 国产av福利第一精品| 国产精品无码嫩草地址更新| 97久久国产亚洲精品超碰热| 人人玩人人添人人澡超碰偷拍| 成人网站精品久久久久|