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PHYKPL Antibody

  • 中文名稱:
    PHYKPL兔多克隆抗體
  • 貨號:
    CSB-PA550806
  • 規格:
    ¥1100
  • 圖片:
    • Gel: 8%SDS-PAGE, Lysate: 40 μg, Lane: Human lymphoma tissue, Primary antibody: CSB-PA550806(AGXT2L2 Antibody) at dilution 1/500, Secondary antibody: Goat anti rabbit IgG at 1/8000 dilution, Exposure time: 30 seconds
  • 其他:

產品詳情

  • Uniprot No.:
  • 基因名:
    PHYKPL
  • 別名:
    PHYKPL antibody; AGXT2L2 antibody; PP92865-phosphohydroxy-L-lysine phospho-lyase antibody; EC 4.2.3.134 antibody; Alanine--glyoxylate aminotransferase 2-like 2 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse
  • 免疫原:
    Fusion protein of Human AGXT2L2
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen affinity purification
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    -20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB
  • 推薦稀釋比:
    Application Recommended Dilution
    ELISA 1:2000-1:5000
    WB 1:500-1:2000
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Catalyzes the pyridoxal-phosphate-dependent breakdown of 5-phosphohydroxy-L-lysine, converting it to ammonia, inorganic phosphate and 2-aminoadipate semialdehyde.
  • 基因功能參考文獻:
    1. Phosphohydroxylysinuria is due to mutations in the AGXT2L2 gene and the resulting lack of activity of phosphohydroxylysine phospholyase in vivo. PMID: 23242558
  • 相關疾?。?/div>
    Phosphohydroxylysinuria (PHLU)
  • 亞細胞定位:
    Mitochondrion.
  • 蛋白家族:
    Class-III pyridoxal-phosphate-dependent aminotransferase family
  • 數據庫鏈接:

    HGNC: 28249

    OMIM: 614683

    KEGG: hsa:85007

    STRING: 9606.ENSP00000310978

    UniGene: Hs.248746



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