在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. PHYH Antibody

PHYH Antibody

  • 中文名稱：
    PHYH兔多克隆抗體
  • 貨號(hào)：
    CSB-PA017946DSR1HU
  • 規(guī)格：
    ￥440
  • 圖片：
    • Western blot
      All lanes: Phytanoyl-CoA dioxygenase, peroxisomal antibody at 3μg/ml + Mouse liver tissue
      Secondary
      Goat polyclonal to rabbit IgG at 1/10000 dilution
      Predicted band size: 39, 28 kDa
      Observed band size: 39 kDa
  • 其他：

產(chǎn)品詳情

  • 產(chǎn)品名稱：
    Rabbit anti-Homo sapiens (Human) PHYH Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    PHYH
  • 別名：
    LN1 antibody; LNAP1 antibody; LNAP1, mouse, homolog of antibody; OTTHUMP00000019131 antibody; OTTHUMP00000019132 antibody; OTTHUMP00000179083 antibody; OTTHUMP00000216226 antibody; PAHX antibody; PAHX_HUMAN antibody; peroxisomal antibody; PhyH antibody; PHYH1 antibody; Phytanic acid oxidase antibody; phytanoil-CoA alpha hydroxylase antibody; phytanoyl CoA 2 hydroxylase antibody; Phytanoyl CoA 2 oxoglutarate dioxygenase antibody; Phytanoyl CoA alpha hydroxylase antibody; Phytanoyl CoA dioxygenase antibody; Phytanoyl CoA dioxygenase peroxisomal antibody; Phytanoyl-CoA alpha-hydroxylase antibody; Phytanoyl-CoA dioxygenase antibody; RD antibody
  • 宿主：
    Rabbit
  • 反應(yīng)種屬：
    Human, Mouse
  • 免疫原：
    Recombinant Human Phytanoyl-CoA dioxygenase, peroxisomal protein (1-338AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標(biāo)記方式：
    Non-conjugated
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
  • 產(chǎn)品提供形式：
    Liquid
  • 應(yīng)用范圍：
    ELISA, WB
  • 推薦稀釋比：
    Application Recommended Dilution
    WB 1:500-1:5000
  • Protocols：
  • 儲(chǔ)存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能：
    Catalyzes the 2-hydroxylation of not only racemic phytanoyl-CoA and the isomers of 3-methylhexadecanoyl-CoA, but also a variety of other mono-branched 3-methylacyl-CoA esters (with a chain length of at least seven carbon atoms) and straight-chain acyl-CoA esters (with a chain length longer than four carbon atoms). Does not hydroxylate long and very long straight chain acyl-CoAs or 2-methyl- and 4-methyl-branched acyl-CoAs.
  • 基因功能參考文獻(xiàn)：
    1. 3 heterozygous variants: c.85C>T (p.Pro29Ser), c.135-2A>G, and c.768del63bp (p.Phe257Glnfs*16) were found in a family with Refsum's disease. PMID: 28681609
    2. substrate specificity of PAHX is broader than expected, so Refsum disease might be characterized by an accumulation of not only phytanic acid but also other 3-alkyl-branched fatty acids PMID: 12923223
    3. Ten novel PHYH mutations found in Refsum disease patients. PMID: 14974078
    4. demonstrate that both unprocessed and processed forms are able to hydroxylate a range of CoA derivatives; site-directed mutagenesis was used to support proposals for the identity of the iron binding istes of PAHX PMID: 15930519
    5. manner in which phytanoyl-CoA 2-hydroxylase (PAHX) binds to iron(II) and 2-oxoglutarate at its active site distinguishes it from that of the other human 2-oxoglutarate (2OG)-dependent oxygenase PMID: 16186124
    6. In the absence of elevated phytanic acid concentrations, clinical neurologic abnormalities in heterozygous relatives of Refsum patients are not attributable to heterozygosity for PAHX mutations. PMID: 18612766

    顯示更多

    收起更多

  • 相關(guān)疾病：
    Refsum disease (RD)
  • 亞細(xì)胞定位：
    Peroxisome.
  • 蛋白家族：
    PhyH family
  • 組織特異性：
    Expressed in liver, kidney, and T-cells, but not in spleen, brain, heart, lung and skeletal muscle.
  • 數(shù)據(jù)庫(kù)鏈接：

    HGNC: 8940

    OMIM: 266500

    KEGG: hsa:5264

    STRING: 9606.ENSP00000263038

    UniGene: Hs.498732



主站蜘蛛池模板： 亚洲欧美国产毛片在线| 中文字幕无码乱码人妻系列蜜桃 | 中文字幕av无码不卡| 天美传媒精品1区2区3区| 内谢少妇xxxxx8老少交| 久久久久国产精品熟女影院| 久久久久久免费毛片精品| 久久午夜夜伦鲁鲁片免费无码影视 | 国产精品a成v人在线播放| 国产露脸精品产三级国产av| 国产乱码一区二区三区爽爽爽 | 亚洲aⅴ无码成人网站国产app | 久久天堂av综合合色蜜桃网| av天堂午夜精品蜜臀av| 国产精品18久久久久久vr| а√天堂8资源中文在线| 2020久久国产综合精品swag| 亚洲午夜久久久精品影院| 狠狠色综合7777久夜色撩人ⅰ | 人禽无码视频在线观看| 国产免费午夜福利在线播放11| 亚洲乱码日产精品bd在观看 | 精品国产一区av天美传媒| 黑人巨大videos精品| 午夜福利av无码一区二区| 成人精品视频一区二区| 国产美足白丝榨精在线观看sm| 伊人色综合网久久天天| 精品人妻无码一区二区色欲产成人 | 成人午夜福利视频| 女人张开腿让男桶喷水高潮| 国产精品人成在线播放新网站| 天码人妻一区二区三区| 亚洲爆乳大丰满无码专区| 亚洲aⅴ无码专区在线观看| 欧美日韩视频在线第一区| 成年女人毛片免费视频| 男女真人国产牲交a做片野外| 日本高清www无色夜在线视频| 午夜精品一区二区三区在线观看| 国产av激情无码久久|