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NDUFAF3 Antibody, FITC conjugated

  • 中文名稱:
    NDUFAF3兔多克隆抗體, FITC偶聯
  • 貨號:
    CSB-PA880103LC01HU
  • 規格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) NDUFAF3 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    NDUFAF3
  • 別名:
    tibody; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 antibody; NDUF3_HUMAN antibody; ndufaf3 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 protein (91-184AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式:
    Liquid
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Essential factor for the assembly of mitochondrial NADH:ubiquinone oxidoreductase complex (complex I).
  • 基因功能參考文獻:
    1. Mutations in NDUFAF3 (C3ORF60), encoding an NDUFAF4 (C6ORF66)-interacting complex I assembly protein, cause fatal neonatal mitochondrial disease. PMID: 19463981
    2. Describes a similar transcript in rat, and compares it to human and mouse transcripts. PMID: 9349717
    3. Describes a similar transcript in mouse. PMID: 12653254
  • 相關疾?。?/div>
    Mitochondrial complex I deficiency (MT-C1D)
  • 亞細胞定位:
    Nucleus. Mitochondrion inner membrane.
  • 數據庫鏈接:

    HGNC: 29918

    OMIM: 252010

    KEGG: hsa:25915

    STRING: 9606.ENSP00000323076

    UniGene: Hs.31387



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