在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. MMADHC Antibody, FITC conjugated

MMADHC Antibody, FITC conjugated

  • 中文名稱：
    MMADHC兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA875665LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) MMADHC Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    MMADHC
  • 別名：
    C2orf25 antibody; cblD antibody; Chromosome 2 open reading frame 25 antibody; CL25022 antibody; Methylmalonic aciduria (cobalamin deficiency) cblD type; with homocystinuria antibody; Methylmalonic aciduria and homocystinuria type D protein antibody; methylmalonic aciduria and homocystinuria type D protein; mitochondrial antibody; mitochondrial antibody; MMAD_HUMAN antibody; Mmadhc antibody; Protein C2orf25; mitochondrial antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Methylmalonic aciduria and homocystinuria type D protein, mitochondrial protein (26-142AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Involved in cobalamin metabolism and trafficking. Plays a role in regulating the biosynthesis and the proportion of two coenzymes, methylcob(III)alamin (MeCbl) and 5'-deoxyadenosylcobalamin (AdoCbl). Promotes oxidation of cob(II)alamin bound to MMACHC. The processing of cobalamin in the cytosol occurs in a multiprotein complex composed of at least MMACHC, MMADHC, MTRR (methionine synthase reductase) and MTR (methionine synthase) which may contribute to shuttle safely and efficiently cobalamin towards MTR in order to produce methionine.
  • 基因功能參考文獻：
    1. analysis of crystal structure of the globular C-terminal domain of human CblD, which is sufficient for its interaction with MMADHC or CblC, and for supporting the cytoplasmic cobalamin trafficking pathway PMID: 26364851
    2. specific regions of MMADHC are involved in differential regulation of adenosylcobalamin and methylcobalamin synthesis PMID: 24722857
    3. MMADHC mutations are associated with methylmalonic aciduria and homocystinuria. PMID: 22156578
    4. mutations in a gene designated MMADHC (currently named C2orf25) are responsible for the cblD defect in vitamin B12 metabolism; various mutations are associated with each of the three biochemical phenotypes of the disorder PMID: 18385497
  • 相關疾病：
    Methylmalonic aciduria and homocystinuria type cblD (MMAHCD)
  • 亞細胞定位：
    Cytoplasm. Mitochondrion.
  • 組織特異性：
    Widely expressed at high levels.
  • 數據庫鏈接：

    HGNC: 25221

    OMIM: 277410

    KEGG: hsa:27249

    STRING: 9606.ENSP00000301920

    UniGene: Hs.5324



主站蜘蛛池模板： 校园春色~综合网| 欧美精品videosex极品| 尹人香蕉久久99天天拍久女久| 国产免费看又黄又大又污的胸| 亚洲丁香五月激情综合| 国产免费午夜a无码v视频| 无码毛片视频一区二区本码 | 大战熟女丰满人妻av| 国产精品美脚玉足脚交| 久久影院午夜伦手机不四虎卡| 两口子交换真实刺激高潮| 深夜福利啪啪片| 日本一道本高清一区二区| 午夜亚洲精品久久一区二区| 久久久久成人精品无码| 亚洲三区在线观看内射后入| 国产精品一区二区手机在线观看 | 女人被强╳到高潮喷水在线观看| 人妻无码一区二区不卡无码av| 国产欧美在线一区二区三| 人妻无码熟妇乱又伦精品视频| 国产精品第12页| 四川老熟女下面又黑又肥| 欧美牲交视频免费观看| 久久精品国产网红主播| 99久久亚洲精品日本无码| 少女韩国电视剧在线观看完整| 中文字幕av久久激情亚洲精品| www一区二区乱码www| 在线 | 一区二区三区四区| 色综合色狠狠天天综合色| 午夜福利国产成人a∨在线观看| 人妻熟妇乱又伦精品hd| 成人性生交大片免费看r链接| 97人妻无码一区| 国产精品美女久久久久网站浪潮| 成人性做爰aaa片免费看不忠| 人妻洗澡被强公日日澡| 在线看片免费人成视频国产片| 亚洲自偷精品视频自拍| 久久亚洲一区二区三区四区五区|