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MARS2 Antibody, FITC conjugated

  • 中文名稱:
    MARS2兔多克隆抗體, FITC偶聯
  • 貨號:
    CSB-PA836221LC01HU
  • 規格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) MARS2 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    MARS2
  • 別名:
    mars2 antibody; Methionine tRNA ligase 2 antibody; Methionine tRNA ligase 2 mitochondrial antibody; Methionine tRNA ligase antibody; Methionine tRNA synthetase 2 antibody; Methionine--tRNA ligase antibody; Methionyl tRNA synthetase 2 mitochondrial antibody; Methionyl tRNA synthetase mitochondrial antibody; Methionyl-tRNA synthetase 2 antibody; MetRS antibody; mitochondrial antibody; Mitochondrial methionine tRNA ligase antibody; Mitochondrial methionyl tRNA synthetase antibody; Mitochondrial methionyl-tRNA synthetase antibody; MtMetRS antibody; SYMM_HUMAN antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Methionine--tRNA ligase, mitochondrial protein (225-460AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式:
    Liquid
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 基因功能參考文獻:
    1. Novel, compound heterozygous, single-nucleotide variants in MARS2 associated with developmental delay, poor growth, and sensorineural hearing loss PMID: 25754315
    2. MARS2 is mutated in Autosomal Recessive Spastic Ataxia with Leukoencephalopathy patients. PMID: 22448145
    3. Sequence analysis of mitochondrial MetRS indicates that this protein contains consensus motifs characteristic of class I aminoacyl-tRNA synthetase but lacks Zn2+ binding motif and C-terminal dimerization region found in MetRSs from various organisms. PMID: 15274629
  • 相關疾病:
    Spastic ataxia 3, autosomal recessive (SPAX3); Combined oxidative phosphorylation deficiency 25 (COXPD25)
  • 亞細胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Class-I aminoacyl-tRNA synthetase family
  • 數據庫鏈接:

    HGNC: 25133

    OMIM: 609728

    KEGG: hsa:92935

    STRING: 9606.ENSP00000282276

    UniGene: Hs.744330



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