在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

LAMB2 Antibody

  • 中文名稱:
    LAMB2兔多克隆抗體
  • 貨號:
    CSB-PA14279A0Rb
  • 規格:
    ¥440
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) LAMB2 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
  • 別名:
    Lamb2 antibody; LAMB2_HUMAN antibody; Laminin B1s chain antibody; Laminin beta 2 antibody; laminin S antibody; Laminin subunit beta 2 antibody; Laminin subunit beta-2 antibody; laminin; beta 2 (laminin S) antibody; Laminin-11 subunit beta antibody; Laminin-14 subunit beta antibody; Laminin-15 subunit beta antibody; Laminin-3 subunit beta antibody; Laminin-4 subunit beta antibody; Laminin-7 subunit beta antibody; Laminin-9 subunit beta antibody; LAMS antibody; NPHS5 antibody; S laminin antibody; S-LAM beta antibody; S-laminin subunit beta antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Laminin subunit beta-2 protein (1530-1798AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,LAMB2 Antibody (CSB-PA14279A0Rb),的標記方式是Non-conjugated。對于LAMB2 Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA14279B0Rb LAMB2 Antibody, HRP conjugated ELISA
    FITC CSB-PA14279C0Rb LAMB2 Antibody, FITC conjugated
    Biotin CSB-PA14279D0Rb LAMB2 Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Binding to cells via a high affinity receptor, laminin is thought to mediate the attachment, migration and organization of cells into tissues during embryonic development by interacting with other extracellular matrix components.
  • 基因功能參考文獻:
    1. In conclusion, we reported three Chinese cases with different LAMB2 mutations and different phenotypes, further broadening the range of eye and kidney pathology associated with mutations in LAMB2. PMID: 27925579
    2. No pathogenic LAMB2 mutations were found in the cohort of children with steroid-resistant focal segmental glomerulosclerosis. PMID: 24856380
    3. Comprehensive gene sequencing revealed a novel LAMB2 variant (c.440A --> G; His147R) that was homozygous in the 9 living, affected family members, observed at a frequency of 2.1% in the Old Order Mennonite population, and absent in 91 non-Mennonite controls PMID: 21236492
    4. Novel mutations in steroid-resistant nephrotic syndrome diagnosed in Tunisian children were detected in LAMB2. PMID: 21125408
    5. All previously reported and several novel LAMB2 mutations in relation to the associated phenotype in patients from 39 unrelated families, are reviewed. PMID: 20556798
    6. Deficiency in LAMB2 causes congenital nephrosis with mesangial sclerosis and distinct eye abnormalities. PMID: 15367484
    7. Hepalaminin, an autoantigen from chronic hepatitis C, consists of two domains of laminin beta-2 and a specific domain. PMID: 15603881
    8. Mutations in the LAMB2 gene encoding laminin beta2, a component of the glomerular basement membrane and the neuro-muscular junction are responsible for the characteristic renal and eye abnormalities of Pierson syndrome. PMID: 16898484
    9. Recessive missense mutations in LAMB2 expand the clinical spectrum of LAMB2-associated disorders. PMID: 16912710
    10. LAMB2 has to be considered as culprit of milder disorders including nephrosis and variable ocular anomalies. PMID: 16921188
    11. We demonstrated that overabundance of the beta2 chain of laminin is associated with increased basement membrane thickness and is possibly related to spermatogenic dysfunction PMID: 17804866
    12. Milder phenotypes of Pearson Syndrome may be related to hypomorphic LAMB2 alleles. PMID: 17943323
    13. Pierson syndrome is defined by the association of mental retardation, microcoria and DMS caused by mutation in LAMB2 gene PMID: 18065803
    14. Study excluded LAMB2 as a candidate gene for Galloway-Mowat syndrome. PMID: 18594871
    15. Loss-of-function mutations in laminin beta2 (LAMB2) cause a broad range of ocular pathology, emphasizing the importance of laminin beta2 in eye development. PMID: 18672223

    顯示更多

    收起更多

  • 相關疾?。?/div>
    Pierson syndrome (PIERSS); Nephrotic syndrome 5 with or without ocular abnormalities (NPHS5)
  • 亞細胞定位:
    Secreted, extracellular space, extracellular matrix, basement membrane. Note=S-laminin is concentrated in the synaptic cleft of the neuromuscular junction.
  • 數據庫鏈接:

    HGNC: 6487

    OMIM: 150325

    KEGG: hsa:3913

    STRING: 9606.ENSP00000307156

    UniGene: Hs.439726



主站蜘蛛池模板: 国产精品美女久久久久av爽李琼 | 精品国产18久久久久久| 国产成人无码精品久久久免费 | 成人精品视频一区二区三区尤物| a在线亚洲男人的天堂| 亚洲国产精品自在拍在线播放蜜臀| 久久久久麻豆v国产精华液好用吗| 精品人伦一区二区三区蜜桃免费| 青青草av一区二区三区| 国产成人18黄网站在线观看| 五月综合激情婷婷六月色窝| 精品人妻av区| 亚洲中文字幕无码mv| 中文字幕日韩人妻不卡一区| 欧美日韩不卡合集视频| 日本最新免费二区三区| 亚洲成在人线av品善网好看| 亚洲sm另类一区二区三区| 手机在线看永久av片免费| 欧美性xxxx狂欢老少配| 欧美专区日韩视频人妻| 五 月 丁 香 综合中文| 天天躁日日躁狠狠躁av麻豆| 国产a国产片国产| 人妻无码vs中文字幕久久av爆| 久久国产加勒比精品无码 | 亚洲欲色欲色xxxxx在线观看| 欧美黑人激情性久久| 人妻体内射精一区二区三区| 5x性社区免费视频播| 亚洲欧美日韩国产综合在线一区| 青青草国产免费国产是公开| 天天狠天天透天干天天怕∴| 成人性生交大片免费看vr| 一本久久伊人热热精品中文字幕 | 日韩在线成年视频人网站观看| 韩日午夜在线资源一区二区| 亚洲一卡2卡三卡四卡精品| 成人av片在线观看免费| 毛片免费全部播放无码| 国产精品成人a区在线观看|