在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

LAMB2 Antibody

  • 中文名稱:
    LAMB2兔多克隆抗體
  • 貨號:
    CSB-PA14279A0Rb
  • 規格:
    ¥440
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) LAMB2 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
  • 別名:
    Lamb2 antibody; LAMB2_HUMAN antibody; Laminin B1s chain antibody; Laminin beta 2 antibody; laminin S antibody; Laminin subunit beta 2 antibody; Laminin subunit beta-2 antibody; laminin; beta 2 (laminin S) antibody; Laminin-11 subunit beta antibody; Laminin-14 subunit beta antibody; Laminin-15 subunit beta antibody; Laminin-3 subunit beta antibody; Laminin-4 subunit beta antibody; Laminin-7 subunit beta antibody; Laminin-9 subunit beta antibody; LAMS antibody; NPHS5 antibody; S laminin antibody; S-LAM beta antibody; S-laminin subunit beta antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Laminin subunit beta-2 protein (1530-1798AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,LAMB2 Antibody (CSB-PA14279A0Rb),的標記方式是Non-conjugated。對于LAMB2 Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA14279B0Rb LAMB2 Antibody, HRP conjugated ELISA
    FITC CSB-PA14279C0Rb LAMB2 Antibody, FITC conjugated
    Biotin CSB-PA14279D0Rb LAMB2 Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Binding to cells via a high affinity receptor, laminin is thought to mediate the attachment, migration and organization of cells into tissues during embryonic development by interacting with other extracellular matrix components.
  • 基因功能參考文獻:
    1. In conclusion, we reported three Chinese cases with different LAMB2 mutations and different phenotypes, further broadening the range of eye and kidney pathology associated with mutations in LAMB2. PMID: 27925579
    2. No pathogenic LAMB2 mutations were found in the cohort of children with steroid-resistant focal segmental glomerulosclerosis. PMID: 24856380
    3. Comprehensive gene sequencing revealed a novel LAMB2 variant (c.440A --> G; His147R) that was homozygous in the 9 living, affected family members, observed at a frequency of 2.1% in the Old Order Mennonite population, and absent in 91 non-Mennonite controls PMID: 21236492
    4. Novel mutations in steroid-resistant nephrotic syndrome diagnosed in Tunisian children were detected in LAMB2. PMID: 21125408
    5. All previously reported and several novel LAMB2 mutations in relation to the associated phenotype in patients from 39 unrelated families, are reviewed. PMID: 20556798
    6. Deficiency in LAMB2 causes congenital nephrosis with mesangial sclerosis and distinct eye abnormalities. PMID: 15367484
    7. Hepalaminin, an autoantigen from chronic hepatitis C, consists of two domains of laminin beta-2 and a specific domain. PMID: 15603881
    8. Mutations in the LAMB2 gene encoding laminin beta2, a component of the glomerular basement membrane and the neuro-muscular junction are responsible for the characteristic renal and eye abnormalities of Pierson syndrome. PMID: 16898484
    9. Recessive missense mutations in LAMB2 expand the clinical spectrum of LAMB2-associated disorders. PMID: 16912710
    10. LAMB2 has to be considered as culprit of milder disorders including nephrosis and variable ocular anomalies. PMID: 16921188
    11. We demonstrated that overabundance of the beta2 chain of laminin is associated with increased basement membrane thickness and is possibly related to spermatogenic dysfunction PMID: 17804866
    12. Milder phenotypes of Pearson Syndrome may be related to hypomorphic LAMB2 alleles. PMID: 17943323
    13. Pierson syndrome is defined by the association of mental retardation, microcoria and DMS caused by mutation in LAMB2 gene PMID: 18065803
    14. Study excluded LAMB2 as a candidate gene for Galloway-Mowat syndrome. PMID: 18594871
    15. Loss-of-function mutations in laminin beta2 (LAMB2) cause a broad range of ocular pathology, emphasizing the importance of laminin beta2 in eye development. PMID: 18672223

    顯示更多

    收起更多

  • 相關疾?。?/div>
    Pierson syndrome (PIERSS); Nephrotic syndrome 5 with or without ocular abnormalities (NPHS5)
  • 亞細胞定位:
    Secreted, extracellular space, extracellular matrix, basement membrane. Note=S-laminin is concentrated in the synaptic cleft of the neuromuscular junction.
  • 數據庫鏈接:

    HGNC: 6487

    OMIM: 150325

    KEGG: hsa:3913

    STRING: 9606.ENSP00000307156

    UniGene: Hs.439726



主站蜘蛛池模板: 轻点好疼好大好爽视频| 欧美乱大交xxxxx潮喷l头像| 在线观看无码av网站永久免费| 久久精品国产9久久综合| 99精品国产在热久久婷婷| 欧美精品一区二区黄a片| 国产成av人片久青草影院| 国产在线看片免费人成视频| 国产suv精品一区二区883| 东京热人妻中文无码av| 亚洲乱色熟女一区二区三区丝袜| 人人揉揉揉香蕉大免费 | 无码精品黑人一区二区三区| 丰满的少妇邻居中文bd| 欧美性色大片在线观看| 琪琪女色窝窝777777| 99国产精品99久久久久久| 国产精品人成视频免费播放| 亚洲日本va在线视频观看| 久久婷婷丁香七月色综合| 久久亚洲一区二区三区四区五区 | 毛片免费全部播放无码| 亚洲欧美日韩国产国产a| 中文字幕av伊人av无码av狼人| 亚洲国产精品国自产拍电影| www国产精品内射老熟女| 国产av无码专区亚洲a∨毛片| 亚洲无av在线中文字幕| 国产98在线 | 欧美| 青青草国产精品人人爱| 动漫av纯肉无码av电影网| 国产影片av级毛片特别刺激| 一边摸一边做爽的视频17国产 | 国产午夜理论不卡在线观看| 国产农村黄aaaaa特黄av毛片| 亚洲综合最新无码专区| 亚洲一区无码中文字幕乱码 | 国产精品久久福利网站| 久久亚洲国产精品成人av秋霞| 一本精品中文字幕在线| 亚洲乱亚洲乱妇50p|