在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

IVD Antibody, FITC conjugated

  • 中文名稱:
    IVD兔多克隆抗體, FITC偶聯(lián)
  • 貨號:
    CSB-PA011921LC01HU
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) IVD Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    IVD
  • 別名:
    ACAD2 antibody; FLJ12715 antibody; FLJ34849 antibody; Isovaleryl CoA dehydrogenase antibody; Isovaleryl CoA dehydrogenase, mitochondrial antibody; Isovaleryl Coenzyme A dehydrogenase antibody; Isovaleryl-CoA dehydrogenase antibody; IVD antibody; IVD_HUMAN antibody; mitochondrial antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Isovaleryl-CoA dehydrogenase, mitochondrial protein (139-241AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評價

靶點詳情

  • 功能:
    Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway. To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as pentanoyl-CoA, hexenoyl-CoA and butenoyl-CoA.
  • 基因功能參考文獻:
    1. Nine novel isovaleryl-CoA dehydrogenase mutations have been found in a Spanish cohort with isovaleric acidemia. PMID: 27904153
    2. Our results have illustrated the heterogeneous mutation spectrum and clinical presentation of IVA in the Japanese patients PMID: 26018748
    3. kinetics and ligand binding of isovaleryl-CoA dehydrogenase PMID: 25450250
    4. study reports the first Saudi isovaleric acidemia patients from a consanguineous family with a novel transversion (p.G362V) and briefly discuss likely phenotype-genotype correlation of the disease in the Saudi population PMID: 23063737
    5. A heterogeneous mutation spectrum in the IVD gene was identified in isovaleric acidemia patients in the United Arab Emirates. PMID: 22960500
    6. All were homozygous for a single c.367 G > A (p.G123R) mutation. Despite the genetic homogeneity of this South African group, the clinical presentation varied, ranging from mental handicap and episodes of metabolic derangement to an asymptomatic state PMID: 22350545
    7. A child with isovaleric acidemia was subsequently found to harbour a known missense mutation (c.A1199G [p.Y371C]) and a novel 4-bp duplication (c.1148_1151dupGCTA [p.Y355X]) in the IVD gene. The former may be a founder mutation in the Chinese population. PMID: 20519759
    8. Replacement of the catalytic glutamate in either short-chain acyl-CoA dehydrogenase (SCAD) or isovaleryl-CoA dehydrogenase (IVD)with glycine resulted in a several-fold reduction in affinity for substrate. PMID: 16376132
    9. Mutations of isovaleryl-CoA dehydrogenase gene is associated with isovaleric acidemia PMID: 17576084

    顯示更多

    收起更多

  • 相關(guān)疾?。?/div>
    Isovaleric acidemia (IVA)
  • 亞細胞定位:
    Mitochondrion matrix.
  • 蛋白家族:
    Acyl-CoA dehydrogenase family
  • 數(shù)據(jù)庫鏈接:

    HGNC: 6186

    OMIM: 243500

    KEGG: hsa:3712

    STRING: 9606.ENSP00000418397

    UniGene: Hs.513646



主站蜘蛛池模板: 夜夜欢天天干| 亚洲—本道 在线无码av发| 大胸美女污污污www网站| 九九综合va免费看| 爱做久久久久久| 18禁黄无遮挡网站免费| 免费看女人与公拘交酡过程| 玩两个丰满老熟女久久网| 波多野结衣av无码久久一区| 青草视频在线观看视频| 色一乱一伦一图一区二区精品| 92精品成人国产在线观看| 欧美黑人大战白嫩在线| 大伊香蕉精品视频在线天堂| 亚洲高清无码加勒比| 99久久国产露脸精品竹菊传媒| 真实的国产乱xxxx| 久久天天躁夜夜躁狠狠躁2022| 色一情一乱一伦一区二区三区小说 | 国产精品无码一区二区三区在| 欧美又大又硬又粗bbbbb| 久久精品国产精品亚洲下载| 97色伦97色伦国产欧美| 亚洲精品毛片一区二区三区| 国产欧美熟妇另类久久久| 欧美片内射欧美美美妇| 无码少妇一区二区浪潮av| 国产乱子伦精品无码专区| 欧亚精品一区三区免费| 免费国产黄网站在线观看可以下载| 肥臀熟女一区二区三区| 老熟女毛茸茸浓毛| 亚洲精品无码你懂的| 亚洲综合久久一本久道| 欧美精品久久久久久久自慰| 狠狠色狠狠人格综合| 精品国产自在现线电影| 桃花色综合影院| 亚洲中文字幕无码久久2020| 日本高清无卡码一区二区 | 扒开双腿吃奶呻吟做受视频 |