在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. HIBCH Antibody

HIBCH Antibody

  • 中文名稱：
    HIBCH兔多克隆抗體
  • 貨號：
    CSB-PA010347GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    HIBCH
  • 別名：
    3 hydroxyisobutyryl Coenzyme A hydrolase antibody; 3 hydroxyisobutyryl Coenzyme A hydrolase; mitochondrial antibody; 3-hydroxyisobutyryl-CoA hydrolase antibody; 3-hydroxyisobutyryl-coenzyme A hydrolase antibody; BETA HYDROXYISOBUTYRYL COENZYME A HYDROLASE antibody; HIB CoA hydrolase antibody; HIB-CoA hydrolase antibody; HIBCH antibody; HIBCH_HUMAN antibody; HIBCoA hydrolase antibody; HIBYL CoA H antibody; HIBYL CoAH antibody; HIBYL-CoA-H antibody; HIBYLCoA H antibody; HIBYLCoAH antibody; mitochondrial antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human HIBCH
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA.
  • 基因功能參考文獻：
    1. Novel (founder) mutation in HIBCH that causes a mild phenotype, allowing survival into adulthood. PMID: 27400804
    2. Polymorphism in HIBCH is associated with HIBCH deficiency. PMID: 27132595
    3. findings demonstrated a novel homozygous pathogenic missense mutation c.950G PMID: 24299452
    4. Molecular analysis in both patients uncovered mutations in the HIBCH gene, including one missense mutation in a conserved part of the protein and two mutations affecting splicing. PMID: 17160907
  • 相關疾病：
    3-hydroxyisobutryl-CoA hydrolase deficiency (HIBCHD)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    Enoyl-CoA hydratase/isomerase family
  • 組織特異性：
    Highly expressed in liver and kidney, also detected in heart, muscle and brain (at protein level). Not detected in lung.
  • 數據庫鏈接：

    HGNC: 4908

    OMIM: 250620

    KEGG: hsa:26275

    STRING: 9606.ENSP00000352706

    UniGene: Hs.656685



主站蜘蛛池模板： 亚洲精品乱码久久久久久自慰| 四房播色综合久久婷婷| 亚洲乱码中文论理电影| av一区二区三区人妻少妇| 无码人妻少妇久久中文字幕蜜桃| 国产全是老熟女太爽了| 少妇爆乳无码专区| 无码成人aaaaa毛片| 国产在线一区二区av视频| 午夜男女无遮掩免费视频| 五十路熟妇高熟无码视频 | 欧美日韩亚洲国产精品| 国产农村乱对白刺激视频| 久久婷婷丁香七月色综合| 午夜福利视频1692| 亚洲性啪啪无码av天堂| 无码人妻久久一区二区三区| 久久大蕉香蕉免费| 成熟妇女性成熟满足视频| 精品综合久久久久久888蜜芽| 久久精品人妻少妇一区二区三区| 久久久久免费看成人影片| 国产99视频精品免费观看9| 真实国产乱啪福利露脸| 日日鲁鲁鲁夜夜爽爽狠狠| 久久久久日韩精品免费观看| 亚洲不卡1卡2卡三卡入口| 亚洲色大成网站www久久九| 亚洲∧v久久久无码精品| 欧美人妻体内射射| 欧美日韩国产综合新一区| 久久久精品波多野结衣| 亚洲国产婷婷香蕉久久久久久| 天天躁日日躁aaaxxⅹ| 国产乱人伦真实精品视频| 国产熟妇与子伦hd| 忍着娇喘人妻被中出中文字幕| 最新69成人精品视频免费| 无码国内精品久久人妻| 欧美人与动牲交zooz乌克兰 | 国产又色又爽无遮挡免费|