在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. HADHB Antibody

HADHB Antibody

  • 中文名稱：
    HADHB兔多克隆抗體
  • 貨號：
    CSB-PA03035A0Rb
  • 規格：
    ￥440
  • 圖片：
    • Immunohistochemistry of paraffin-embedded human prostate tissue using CSB-PA03035A0Rb at dilution of 1:50
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) HADHB Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    HADHB
  • 別名：
    2 enoyl Coenzyme A (CoA) hydratase beta subunit antibody; 3 ketoacyl Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein beta subunit antibody; 3 ketoacyl Coenzyme A thiolase antibody; 3 ketoacyl Coenzyme A thiolase of mitochondrial trifunctional protein beta subunit antibody; 3-ketoacyl-CoA thiolase antibody; Acetyl CoA acyltransferase antibody; Acetyl-CoA acyltransferase antibody; Beta ketothiolase antibody; Beta-ketothiolase antibody; ECHB antibody; ECHB_HUMAN antibody; HADH antibody; Hadhb antibody; Hydroxyacyl CoA dehydrogenase/3 ketoacyl CoA thiolase/enoyl CoA hydratase (trifunctional protein); beta subunit antibody; Hydroxyacyl Coenzyme A (CoA) dehydrogenase beta subunit antibody; Hydroxyacyl Coenzyme A dehydrogenase antibody; Hydroxyacyl Coenzyme A dehydrogenase beta subunit antibody; Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) beta subunit antibody; MGC87480 antibody; Mitochondrial trifunctional enzyme beta subunit antibody; Mitochondrial trifunctional protein beta subunit antibody; MSTP 029 antibody; MSTP029 antibody; MTPB antibody; TP beta antibody; TP-beta antibody; TPbeta antibody; Trifunctional enzyme subunit beta antibody; Trifunctional enzyme subunit beta mitochondrial antibody; Trifunctional protein antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Trifunctional enzyme subunit beta, mitochondrial protein (35-283AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    Non-conjugated

    本頁面中的產品，HADHB Antibody (CSB-PA03035A0Rb)，的標記方式是Non-conjugated。對于HADHB Antibody，我們還提供其他標記。見下表：

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA03035B0Rb HADHB Antibody, HRP conjugated ELISA
    FITC CSB-PA03035C0Rb HADHB Antibody, FITC conjugated
    Biotin CSB-PA03035D0Rb HADHB Antibody, Biotin conjugated ELISA
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA, IHC
  • 推薦稀釋比：
    Application Recommended Dilution
    IHC 1:20-1:200
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Mitochondrial trifunctional enzyme catalyzes the last three of the four reactions of the mitochondrial beta-oxidation pathway. The mitochondrial beta-oxidation pathway is the major energy-producing process in tissues and is performed through four consecutive reactions breaking down fatty acids into acetyl-CoA. Among the enzymes involved in this pathway, the trifunctional enzyme exhibits specificity for long-chain fatty acids. Mitochondrial trifunctional enzyme is a heterotetrameric complex composed of two proteins, the trifunctional enzyme subunit alpha/HADHA carries the 2,3-enoyl-CoA hydratase and the 3-hydroxyacyl-CoA dehydrogenase activities, while the trifunctional enzyme subunit beta/HADHB described here bears the 3-ketoacyl-CoA thiolase activity.
  • 基因功能參考文獻：
    1. Mutations in HADHB, which encodes the beta-subunit of mitochondrial trifunctional protein, cause infantile onset hypoparathyroidism and peripheral polyneuropathy. PMID: 24664533
    2. Heterozygous mutation in HADHB gene cause early-onset axonal axonal Charcot-Marie-tooth disease. PMID: 24314034
    3. mutational analysis of the HADHB gene, which encodes long-chain 3-ketoacyl-CoA thiolase, identified compound heterozygous mutations of c.520C>T (p.R141C) and c.1331G>A (p.R411K) in a case of mitochondrial trifunctional protein deficiency PMID: 22000755
    4. The present findings showed that all missense mutations in HADHB were disease-causing. PMID: 19699128
    5. HADHB trifunctional enzyme, human renin, and poly(C)-binding protein are novel renin mRNA-binding proteins that target a cis-element in the 3'-UTR of renin mRNA and regulate renin production PMID: 12933794
    6. The common disease causing mutation of G1528C in MTP gene in caucasian in probably not a common mutation in Chinese Han people in Beijing. PMID: 17199921

    顯示更多

    收起更多

  • 相關疾病：
    Mitochondrial trifunctional protein deficiency (MTPD)
  • 亞細胞定位：
    Mitochondrion. Mitochondrion inner membrane. Mitochondrion outer membrane. Endoplasmic reticulum.
  • 蛋白家族：
    Thiolase family
  • 數據庫鏈接：

    HGNC: 4803

    OMIM: 143450

    KEGG: hsa:3032

    STRING: 9606.ENSP00000325136

    UniGene: Hs.515848



主站蜘蛛池模板： 麻豆视传媒精品av| 成人动漫综合网| 欧美人与动性xxxxx杂性| 少妇真实被内射视频三四区| 东北少妇不戴套对白第一次| 欧美乱大交av片久久123| 捆绑白丝粉色jk震动捧喷白浆| 婷婷综合久久狠狠色99h| 97久久精品人人槡人妻人| 亚洲精品中文字幕无码蜜桃| 日韩av无码精品人妻系列| 国产精品国色综合久久| 国模无码人体一区二区| 成人午夜福利院在线观看| 国产亚洲视频在线观看播放 | 国内熟妇人妻色无码视频在线| 黄瓜视频在线观看网址| 久久av无码αv高潮αv喷吹| 国产精品午夜福利视频234区 | 国产肉体xxxx裸体137大胆| 久久久久久妓女精品影院| 99久久国产亚洲高清观看 | 色狠狠久久av五月综合| 麻豆亚洲国产成人精品无码区| 在线视频 亚太 国产 欧美 一区二区| 无码一区二区三区av免费蜜桃| 四虎精品免费永久免费视频| 一二区成人影院电影网| 国产精品久久久久影院嫩草| 人妻免费一区二区三区最新| 久久青青草原国产精品最新片| 成人亚洲精品777777| 国产老熟妇精品观看| 国产又黄又硬又粗| 免费无遮挡无码视频网站| 欧美 国产 亚洲视频| 免费乱理伦片在线观看八戒| 亚洲精品久久久口爆吞精| 久久亚洲中文字幕无码| 又色又污又爽又黄的网站| 蜜桃网站入口可看18禁|