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Your Good Partner in Biology Research

GYS2 Antibody

  • 中文名稱:
    GYS2兔多克隆抗體
  • 貨號:
    CSB-PA528498
  • 規格:
    ¥1100
  • 圖片:
    • The image on the left is immunohistochemistry of paraffin-embedded Human liver cancer tissue using CSB-PA528498(GYS2 Antibody) at dilution 1/40, on the right is treated with fusion protein. (Original magnification: ×200)
    • The image on the left is immunohistochemistry of paraffin-embedded Human brain tissue using CSB-PA528498(GYS2 Antibody) at dilution 1/40, on the right is treated with fusion protein. (Original magnification: ×200)
  • 其他:

產品詳情

  • Uniprot No.:
  • 基因名:
  • 別名:
    EC 2.4.1.11 antibody; Glycogen [starch] synthase antibody; Glycogen starch synthase liver antibody; Glycogen synthase 2 liver antibody; Gys2 antibody; GYS2_HUMAN antibody; liver antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse,Rat
  • 免疫原:
    Fusion protein of Human GYS2
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen affinity purification
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    -20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,IHC
  • 推薦稀釋比:
    Application Recommended Dilution
    ELISA 1:2000-1:5000
    IHC 1:50-1:200
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Transfers the glycosyl residue from UDP-Glc to the non-reducing end of alpha-1,4-glucan.
  • 基因功能參考文獻:
    1. Mutation in GYS2 gene is associated with hepatic glycogen synthase deficiency. PMID: 28245189
    2. Sequencing of the GYS2 gene is more likely to be positive in patients with fasting ketotic hypoglycaemia and concomitant postprandial hyperglycaemia with hyperlactataemia. PMID: 23426827
    3. The GYS2 gene is a new susceptibility gene that significantly affects the risk for ovary syndrome through obesity-related conditions. PMID: 22951595
  • 相關疾病:
    Glycogen storage disease 0 (GSD0)
  • 蛋白家族:
    Glycosyltransferase 3 family
  • 數據庫鏈接:

    HGNC: 4707

    OMIM: 138571

    KEGG: hsa:2998

    STRING: 9606.ENSP00000261195

    UniGene: Hs.82614



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