在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. GTPBP3 Antibody

GTPBP3 Antibody

  • 中文名稱：
    GTPBP3兔多克隆抗體
  • 貨號：
    CSB-PA010034GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    GTPBP3
  • 別名：
    GTPBP3 antibody; MTGP1 antibody; tRNA modification GTPase GTPBP3 antibody; mitochondrial antibody; GTP-binding protein 3 antibody; Mitochondrial GTP-binding protein 1 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human GTPBP3
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB,IHC
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    GTPase involved in the 5-carboxymethylaminomethyl modification (mnm(5)s(2)U34) of the wobble uridine base in mitochondrial tRNAs.
  • 基因功能參考文獻：
    1. Defects in the mitochondrial tRNA modification enzymes MTO1 and GTPBP3 promote different metabolic reprogramming through a HIF-PPARgamma-UCP2-AMPK axis. PMID: 29348686
    2. GTPBP3 defective expression is associated with an mitochondrial-tRNA hypomodification status.GTPBP3 plays a role in the regulation of UCP2 and MCP1 proteins through AMPK signaling. PMID: 26642043
    3. Most individuals with GTPBP3 mutations developed neurological symptoms and MRI involvement of thalamus, putamen, and brainstem resembling Leigh syndrome. PMID: 25434004
    4. GTPBP3 localizes in the mitochondria and is a deafness-associated homolog of yeast MSS1. PMID: 12370316
    5. Phenotype of non-syndromic deafness associated with the mitochondrial A1555G mutation is modulated by mitochondrial RNA modifying enzymes MTO1 and GTPBP3. PMID: 15542390
    6. Data show that the two most abundant GTPBP3 isoforms exhibit moderate affinity for guanine nucleotides like their bacterial homologue, MnmE, although they hydrolyze GTP at a 100-fold lower rate. PMID: 18852288

    顯示更多

    收起更多

  • 相關疾病：
    Combined oxidative phosphorylation deficiency 23 (COXPD23)
  • 亞細胞定位：
    Mitochondrion.
  • 蛋白家族：
    TRAFAC class TrmE-Era-EngA-EngB-Septin-like GTPase superfamily, TrmE GTPase family
  • 組織特異性：
    Ubiquitously expressed.
  • 數據庫鏈接：

    HGNC: 14880

    OMIM: 580000

    KEGG: hsa:84705

    UniGene: Hs.334885



主站蜘蛛池模板： 日韩中文亚洲欧美视频二| 免费人成视频在线观看播放网站 | 国产成人一区二区三区别 | 日本高清中文字幕免费一区二区| 欧美视频专区一二在线观看| 久久综合伊人77777麻豆| 国产精品国色综合久久| 成人电线在线播放无码 | 亚洲国产精品成人天堂| 国内精品久久久久精免费| 午夜成人性刺激免费视频| 国产成人无码aa精品一区| 特黄特色的大片观看免费视频| 亚洲国产欧美国产综合久久| 亚洲欧美综合精品成人网站| 无码人妻少妇色欲av一区二区 | 亚洲成av人片香蕉片| 国产精品高清视亚洲中文| 国产亚洲人成网站观看| 精品无码久久久久国产| 四虎精品成人免费视频 | 色舞月亚洲综合一区二区| 波多野结衣初尝黑人| 精品人妻少妇一区二区三区| 亚洲成av人片在线观看无码不卡| 亚洲vav在线男人的天堂| 无码精品一区二区三区免费视频| 精品亚洲麻豆1区2区3区| 肉体裸交丰满丰满少妇在线观看| 人妻丰满熟妇av无码处处不卡 | 久久人人爽人人爽人人片dvd| 国内精品久久久久久久影视麻豆| 天天躁日日躁狠狠躁性色avq| 亚洲人成人网站色www| 综合激情亚洲丁香社区| 亚洲hdmi高清线| 永久黄网站色视频免费| 骚女人干起来舒服视频在线| 国产精品亚洲第一区在线观看| 97久久超碰国产精品2021| 精品国产经典三级在线看|