在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. ERCC6L2 Antibody

ERCC6L2 Antibody

  • 中文名稱：
    ERCC6L2兔多克隆抗體
  • 貨號：
    CSB-PA004261LA01HU
  • 規格：
    ￥440
  • 圖片：
    • Immunohistochemistry of paraffin-embedded human lung tissue using CSB-PA004261LA01HU at dilution of 1:100
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) ERCC6L2 Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    ERCC6L2
  • 別名：
    C9orf102 antibody; Chromosome 9 open reading frame 102 antibody; excision repair cross-complementing rodent repair deficiency; complementation group 6-like 2 antibody; FLJ37706 antibody; MGC30192 antibody; MGC43364 antibody; Putative DNA repair and recombination protein RAD26-like antibody; putative repair and recombination helicase RAD26L antibody; RAD26_HUMAN antibody; Rad26l antibody; RAD26L hypothetical protein antibody; SR278 antibody; stretch responsive protein 278 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human DNA excision repair protein ERCC-6-like 2 protein (72-371AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    Non-conjugated

    本頁面中的產品，ERCC6L2 Antibody (CSB-PA004261LA01HU)，的標記方式是Non-conjugated。對于ERCC6L2 Antibody，我們還提供其他標記。見下表：

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA004261LB01HU ERCC6L2 Antibody, HRP conjugated ELISA
    FITC CSB-PA004261LC01HU ERCC6L2 Antibody, FITC conjugated
    Biotin CSB-PA004261LD01HU ERCC6L2 Antibody, Biotin conjugated ELISA
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA, IHC
  • 推薦稀釋比：
    Application Recommended Dilution
    IHC 1:20-1:200
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    May be involved in early DNA damage response.
  • 基因功能參考文獻：
    1. ERCC6L2-associated disorder has recently been described. We identified an additional case through whole-exome sequencing. At the age of 9 years, the patient underwent whole exome sequencing and was discovered to have a homozygous stop mutation in ERCC6L2 (NCBI RefSeq NG_034107.1), c.1687C>T (p.Arg563*). PMID: 29633571
    2. The inherited bone marrow failure syndrome caused by biallelic variants in ERCC6L2 can be considered as a primary transcription deficiency rather than a DNA repair defect PMID: 29987015
    3. Hebo is ubiquitously expressed, localized in the nucleus, and rapidly recruited to DNAdsb's in an NBS1-dependent manner. PMID: 27185855
    4. These observations identify a distinct bone-marrow-failure syndrome due to mutations in ERCC6L2, a gene implicated in DNA repair and mitochondrial function. PMID: 24507776
  • 相關疾病：
    Bone marrow failure syndrome 2 (BMFS2)
  • 亞細胞定位：
    Nucleus. Cytoplasm, cytoskeleton, microtubule organizing center, centrosome. Mitochondrion. Note=Colocalizes with NEK6 in the centrosome. In response to DNA damage, translocates from the cytosol to mitochondria and nucleus in a reactive oxygen species (ROS)-dependent manner.
  • 蛋白家族：
    SNF2/RAD54 helicase family
  • 組織特異性：
    Expressed in bone marrow (at protein level).
  • 數據庫鏈接：

    HGNC: 26922

    OMIM: 615667

    KEGG: hsa:375748

    STRING: 9606.ENSP00000288985

    UniGene: Hs.432364



主站蜘蛛池模板： 久久/这里只精品99re66| 人妻少妇精品无码专区app| 亚洲精品乱码久久久久久久久久久久| 日本妇人成熟免费| 国产精品成人嫩草影院| 国产美女裸身网站免费观看视频| 中国china露脸自拍性hd| 久久这里只有精品18| 亚洲人成电影网站色| 亚洲kkk4444在线观看| 日本丰满少妇bbb| 国产精品va在线观看无码不卡| 凹凸国产熟女精品视频app| 亚洲精品国产电影| 欧洲无码精品a码无人区| √最新版天堂资源网在线下载| 拍摄av现场失控高潮数次| 国产精品情侣呻吟对白视频| 久久亚洲精品ab无码播放| 中文字幕亚洲综合久久综合| 性饥渴少妇av无码毛片| 色噜噜一区二区三区| 丁香五月亚洲综合在线| 少妇饥渴偷公乱av在线观看涩爱| 久久激情五月丁香伊人| 精品人妻系列无码人妻漫画| 柠檬福利精品视频导航| 综合久久—本道中文字幕| 国产乱码精品一区二区三区四川人| 综合无码一区二区三区| 精品蜜臀av在线天堂| 亚洲欧洲日产国码无码网站| 免费人成视频在线观看网站| а√中文在线资源库| 国产精品星空无限传媒| 在线观看午夜亚洲一区| 午夜精品国产精品大乳美女| 国产精品性夜天天拍拍2021| 最新亚洲中文av在线不卡| 精品国产aⅴ无码一区二区| 国内裸体无遮挡免费视频|