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ENO3 Antibody, FITC conjugated

  • 中文名稱:
    ENO3兔多克隆抗體, FITC偶聯(lián)
  • 貨號(hào):
    CSB-PA13169C0Rb
  • 規(guī)格:
    ¥880
  • 其他:

產(chǎn)品詳情

  • 產(chǎn)品名稱:
    Rabbit anti-Homo sapiens (Human) ENO3 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
  • 別名:
    2 phospho D glycerate hydro lyase antibody; 2 phospho D glycerate hydrolyase antibody; 2-phospho-D-glycerate hydro-lyase antibody; Beta enolase antibody; Beta-enolase antibody; ENO3 antibody; ENOB_HUMAN antibody; Enolase 3 (beta muscle) antibody; Enolase 3 antibody; Enolase3 antibody; GSD13 antibody; MSE antibody; Muscle specific enolase antibody; Muscle-specific enolase antibody; Skeletal muscle enolase antibody
  • 宿主:
    Rabbit
  • 反應(yīng)種屬:
    Human
  • 免疫原:
    Recombinant Human Beta-enolase protein (7-432AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標(biāo)記方式:
    FITC
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產(chǎn)品提供形式:
    Liquid
  • 儲(chǔ)存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產(chǎn)品評(píng)價(jià)

靶點(diǎn)詳情

  • 功能:
    Appears to have a function in striated muscle development and regeneration.
  • 基因功能參考文獻(xiàn):
    1. Molecular genetic analysis of ENO3 gene revealed two novel homozygous missense mutations, (p.Asn151Ser and p.Glu187Lys)in patients presenting with recurrent rhabdomyolysis. PMID: 25267339
    2. Pyridoxamine and carnosine protected enolase against the total loss of catalytic activity. PMID: 21347838
  • 相關(guān)疾?。?/div>
    Glycogen storage disease 13 (GSD13)
  • 亞細(xì)胞定位:
    Cytoplasm.
  • 蛋白家族:
    Enolase family
  • 組織特異性:
    The alpha/alpha homodimer is expressed in embryo and in most adult tissues. The alpha/beta heterodimer and the beta/beta homodimer are found in striated muscle, and the alpha/gamma heterodimer and the gamma/gamma homodimer in neurons.
  • 數(shù)據(jù)庫(kù)鏈接:

    HGNC: 3354

    OMIM: 131370

    KEGG: hsa:2027

    STRING: 9606.ENSP00000324105

    UniGene: Hs.224171



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