在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

EBP Antibody

  • 中文名稱:
    EBP兔多克隆抗體
  • 貨號:
    CSB-PA624016EA01HU
  • 規格:
    ¥440
  • 圖片:
    • Western blot
      All lanes: EBP antibody at 2µg/ml
      Lane 1: A549 whole cell lysate
      Lane 2: 293T whole cell lysate
      Secondary
      Goat polyclonal to rabbit IgG at 1/10000 dilution
      Predicted band size: 27 kDa
      Observed band size: 27 kDa
    • Immunohistochemistry of paraffin-embedded human breast cancer using CSB-PA624016EA01HU at dilution of 1:100
    • Immunohistochemistry of paraffin-embedded human lung cancer using CSB-PA624016EA01HU at dilution of 1:100
    • Immunofluorescent analysis of 293T cells using CSB-PA624016EA01HU at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L)
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) EBP Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    EBP
  • 別名:
    EBP; 3-beta-hydroxysteroid-Delta(8,Delta(7-isomerase; Cholestenol Delta-isomerase; Delta(8-Delta(7 sterol isomerase; D8-D7 sterol isomerase; Emopamil-binding protein
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human 3-beta-hydroxysteroid-Delta(8),Delta(7)-isomerase protein (2-230AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,EBP Antibody (CSB-PA624016EA01HU),的標記方式是Non-conjugated。對于EBP Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA624016EB01HU EBP Antibody, HRP conjugated ELISA
    FITC CSB-PA624016EC01HU EBP Antibody, FITC conjugated
    Biotin CSB-PA624016ED01HU EBP Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA, WB, IHC, IF
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:500-1:2000
    IHC 1:20-1:200
    IF 1:50-1:200
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Catalyzes the conversion of Delta(8)-sterols to their corresponding Delta(7)-isomers.
  • 基因功能參考文獻:
    1. This study expands the current phenotypic spectrum of males with hypomorphic EBP mutations and supports to the hypothesis that there exists an X-linked recessive entity independent of CDPX2. PMID: 24700572
    2. Mutation analysis revealed a heterozygous novel missense mutation, c.204G>T (p.W68C), in exon 2. PMID: 24915996
    3. With non-mosaic EBP mutations in males. PMID: 24459067
    4. Report steroidomimetic aminomethyl spiroacetals as novel inhibitors of the enzyme Delta8,7-sterol isomerase in cholesterol biosynthesis. PMID: 24493593
    5. Elastin binding protein and FKBP65 modulate the kinetics of self-assembly of tropoelastin in an in vitro system. PMID: 24106871
    6. Results show a clear relationship between abnormal sterol profile and the EBP gene mutation PMID: 22121851
    7. postzygotic mosaicism on an ichthyosiform skin lesion in the mother of a girl with X-linked dominant chondrodysplasia punctata associated with a novel EBP mutation. PMID: 21931045
    8. Molecular analysis of EBP mutations were made. PMID: 17378690
    9. Emopamil binding protein (EBP)-shRNA sequences were designed and tested for their effectiveness. PMID: 17498944
    10. We found two novel (3G-->T and 419-422delTTCT) and one known mutation in the EBP gene. The strong phenotypic variability in our patients suggests that there is no clear genotype-phenotype correlation. PMID: 17949453
    11. two unrelated Thai girls with chondrodysplasia punctata type 2. Mutation analysis by PCR-sequencing the entire coding region of emopamil binding protein(EBP) successfully revealed two potentially pathogenic, novel mutations, c.616G-->T and c.382delC. PMID: 18573709

    顯示更多

    收起更多

  • 相關疾?。?/div>
    Chondrodysplasia punctata 2, X-linked dominant (CDPX2); MEND syndrome (MEND)
  • 亞細胞定位:
    Endoplasmic reticulum membrane; Multi-pass membrane protein. Nucleus envelope. Cytoplasmic vesicle.
  • 蛋白家族:
    EBP family
  • 數據庫鏈接:

    HGNC: 3133

    OMIM: 300205

    KEGG: hsa:10682

    STRING: 9606.ENSP00000417052

    UniGene: Hs.30619



主站蜘蛛池模板: 欧洲亚洲国产成人综合色婷婷| 无码人妻av一区二区三区蜜臀| 少妇脱了内裤让我添| 亚洲熟妇无码av另类vr影视| 亚洲中文无码av永久伊人| 中文字幕在线精品视频| 亚洲精品自在在线观看| 9re热国产这里只有精品| 国产精品嫩草影院免费观看| 亚洲成av人片在线观看无| 中文字幕人成乱码熟女免费| 久久综合给合久久97色| 亚洲欧美精品午睡沙发| 久久人人爽人人爽人人av东京热 | 乌克兰少妇xxxx做受| 久久婷婷色综合一区二区| 国产av国内精品jk制服| 人妻熟女久久久久久久| 亚洲码欧美码一区二区三区| 少妇愉情理伦片高潮日本| 久久精品国产久精国产果冻传媒| 人妻插b视频一区二区三区| 欧美老妇与zozoz0交| 欧美一性一乱一交一视频| 国产系列丝袜熟女精品网站| 欧美性大战久久久久xxx| 国产精品久久久久久无毒不卡| 久章草国语自产拍在线观看 | 精品人妻无码一区二区色欲产成人| 青青青伊人色综合久久| 欧美黑人巨大videos在线| 巨大乳女人做爰视频在线看| 欧美日本韩国亚洲| 狂野欧美性猛xxxx乱大交| 免费国产成人午夜福利电影| 亚洲综合色无码| 成人亚洲精品久久久久软件| 337p粉嫩日本欧洲亚福利| 亚洲精品久久久久一区二区| 艳妇乳肉豪妇荡乳av无码福利| 97在线成人国产在线视频|