在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. COQ6 Antibody

COQ6 Antibody

  • 中文名稱：
    COQ6兔多克隆抗體
  • 貨號：
    CSB-PA005805GA01HU
  • 規格：
    ￥3,900
  • 其他：

產品詳情

  • Uniprot No.：
  • 基因名：
    COQ6
  • 別名：
    CGI-10 antibody; Coenzyme Q6 homolog (yeast) antibody; Coenzyme Q6 homolog; monooxygenase (S. cerevisiae) antibody; Coenzyme Q6 homolog; monooxygenase (yeast) antibody; coq6 antibody; COQ6_HUMAN antibody; Ubiquinone biosynthesis monooxygenase COQ6 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human,Mouse,Rat
  • 免疫原：
    Human COQ6
  • 免疫原種屬：
    Homo sapiens (Human)
  • 抗體亞型：
    IgG
  • 純化方式：
    Antigen Affinity Purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles.
  • 產品提供形式：
    Liquid
  • 應用范圍：
    ELISA,WB
  • Protocols：
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    FAD-dependent monooxygenase required for the C5-ring hydroxylation during ubiquinone biosynthesis. Catalyzes the hydroxylation of 3-hexaprenyl-4-hydroxybenzoic acid (HHB) to 3-hexaprenyl-4,5-dihydroxybenzoic acid (DHHB). The electrons required for the hydroxylation reaction may be funneled indirectly from NADPH via a ferredoxin/ferredoxin reductase system to COQ6. Is able to perform the deamination reaction at C4 of 3-hexaprenyl-4-amino-5-hydroxybenzoic acid (HHAB) to produce DHHB when expressed in yeast cells lacking COQ9, even if utilization of para-aminobenzoic acid (pABA) involving C4-deamination seems not to occur in bacteria, plants and mammals, where only C5 hydroxylation of HHB has been shown.
  • 基因功能參考文獻：
    1. Primary CoQ10 deficiency due to COQ6 mutations should be considered in children presenting with both Steroid-Resistant Focal Segmental Glomerulosclerosis and sensorineural hearing loss. An early diagnosis of COQ6 mutations is essential because the condition is treatable when CoQ10 supplementation is started at the early stage. PMID: 28117207
    2. Data indicate a heterozygous loss-of-function coenzyme Q10 (CoQ10) biosynthesis monooxygenase 6 gene (COQ6)missense mutation in familial schwannomatosis. PMID: 24763291
    3. COQ6 mutations in human patients produce nephrotic syndrome with sensorineural deafness PMID: 21540551
  • 相關疾病：
    Coenzyme Q10 deficiency, primary, 6 (COQ10D6)
  • 亞細胞定位：
    Mitochondrion inner membrane; Peripheral membrane protein; Matrix side. Golgi apparatus. Cell projection.
  • 蛋白家族：
    UbiH/COQ6 family
  • 組織特異性：
    Widely expressed.
  • 數據庫鏈接：

    HGNC: 20233

    OMIM: 614647

    KEGG: hsa:51004

    STRING: 9606.ENSP00000333946

    UniGene: Hs.131555



主站蜘蛛池模板： 在线欧美中文字幕农村电影| av边做边流奶水无码免费| 人人爽人人爽人人片av亚洲 | 国产成人无码精品久久久性色| 久久久精品2019免费观看 | 久久www免费人成_看片中文| 极品少妇被猛的白浆直喷白浆| 久久精品99国产国产精| 天堂mv在线mv免费mv香蕉| 人妻少妇无码精品专区| 热re99久久精品国产99热| 久久久久久亚洲精品中文字幕| 日韩中文高清在线专区 | 亚洲欧洲日产国码无码| 亚洲熟女乱色综合亚洲小说| 久久午夜电影网| 久久无码高潮喷水抽搐| 国产成人久久av免费| 无码人妻精品一区二区三区在线| 2021国产精品一卡2卡三卡4卡| 天码欧美日本一道免费| 国产精品视频二区不卡| 精品夜夜爽欧美毛片视频| 东京热一精品无码av| 国产无遮挡又爽又黄的视频| 久久不见久久见免费影院www | 欧美黑人粗大xxxxbbbb| av无码中文字幕不卡一区二区三区| 人与嘼av免费| 亚洲欧美色一区二区三区| 国产真实偷乱视频| 国产综合一区二区三区黄页秋霞| 免费看又黄又无码的网站 | 色v99在线影院| 一边啪啪一边呻吟av夜夜嗨| 一本一道人人妻人人妻αv| 国产精品怡红院在线观看| 亚洲桃色天堂网| 99久热re在线精品99re8热视频| 亚洲日韩国产一区二区三区| 亚洲国产成人爱av在线播放|