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CEP89 Antibody

  • 中文名稱:
    CEP89兔多克隆抗體
  • 貨號:
    CSB-PA853505LA01HU
  • 規格:
    ¥440
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) CEP89 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    CEP89
  • 別名:
    CCDC123 antibody; Centrosomal protein 89 kDa antibody; Centrosomal protein of 89 kDa antibody; cep89 antibody; CEP89_HUMAN antibody; Coiled-coil domain-containing protein 123 antibody; Coiled-coil domain-containing protein 123; mitochondrial antibody; FLJ14640 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Centrosomal protein of 89 kDa protein (25-235AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated

    本頁面中的產品,CEP89 Antibody (CSB-PA853505LA01HU),的標記方式是Non-conjugated。對于CEP89 Antibody,我們還提供其他標記。見下表:

    可提供標記
    標記方式 貨號 產品名稱 應用
    HRP CSB-PA853505LB01HU CEP89 Antibody, HRP conjugated ELISA
    FITC CSB-PA853505LC01HU CEP89 Antibody, FITC conjugated
    Biotin CSB-PA853505LD01HU CEP89 Antibody, Biotin conjugated ELISA
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Required for ciliogenesis. Also plays a role in mitochondrial metabolism where it may modulate complex IV activity.
  • 基因功能參考文獻:
    1. CEP89 proteins play an important role in mitochondrial metabolism, especially complex IV activity, and are required for neuronal and cognitive function across evolution. PMID: 23575228
  • 相關疾病:
    Homozygous deletion comprising CEP89 and SLC7A9 genes has been reported in a patient with isolated complex IV deficiency, intellectual disability and multisystemic problems that include cystinuria, cataract, broad based walking pattern and deafness.
  • 亞細胞定位:
    Cytoplasm, cytosol. Cytoplasm, cytoskeleton, microtubule organizing center, centrosome. Cytoplasm, cytoskeleton, spindle pole. Cytoplasm, cytoskeleton, microtubule organizing center, centrosome, centriole. Mitochondrion intermembrane space. Note=Localizes to the distal appendage region of the centriole, which anchors the mother centriole to the plasma membrane.
  • 數據庫鏈接:

    HGNC: 25907

    OMIM: 615470

    KEGG: hsa:84902

    STRING: 9606.ENSP00000306105

    UniGene: Hs.599703



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