在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

  1. Home
  2. 抗體
  3. 多克隆抗體
  4. ALG9 Antibody, FITC conjugated

ALG9 Antibody, FITC conjugated

  • 中文名稱：
    ALG9兔多克隆抗體, FITC偶聯
  • 貨號：
    CSB-PA867161LC01HU
  • 規格：
    ￥880
  • 其他：

產品詳情

  • 產品名稱：
    Rabbit anti-Homo sapiens (Human) ALG9 Polyclonal antibody
  • Uniprot No.：
  • 基因名：
    ALG9
  • 別名：
    ALG9 antibody; ALG9_HUMAN antibody; Alpha-1,2-mannosyltransferase ALG9 antibody; Asparagine-linked glycosylation protein 9 homolog antibody; Disrupted in bipolar disorder protein 1 antibody
  • 宿主：
    Rabbit
  • 反應種屬：
    Human
  • 免疫原：
    Recombinant Human Alpha-1,2-mannosyltransferase ALG9 protein (434-618AA)
  • 免疫原種屬：
    Homo sapiens (Human)
  • 標記方式：
    FITC
  • 克隆類型：
    Polyclonal
  • 抗體亞型：
    IgG
  • 純化方式：
    >95%, Protein G purified
  • 濃度：
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液：
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
  • 產品提供形式：
    Liquid
  • 儲存條件：
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期：
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途：
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能：
    Catalyzes the transfer of mannose from Dol-P-Man to lipid-linked oligosaccharides.
  • 基因功能參考文獻：
    1. ALG9 is upregulated in peripheral blood mononuclear cells of galactosaemia patients. PMID: 26733289
    2. Our study shows that some pathogenic variants in ALG9 can present as a lethal skeletal dysplasia with visceral malformations as the most severe phenotype PMID: 25966638
    3. Due to the ALG9 deficiency, cells accumulated the lipid-linked oligosaccharides Man(6)GlcNAc(2)-PP-dolichol and Man(8)GlcNAc(2)-PP-dolichol. PMID: 19451548
  • 相關疾病：
    Congenital disorder of glycosylation 1L (CDG1L); Gillessen-Kaesbach-Nishimura syndrome (GIKANIS)
  • 亞細胞定位：
    Endoplasmic reticulum membrane; Multi-pass membrane protein.
  • 蛋白家族：
    Glycosyltransferase 22 family
  • 組織特異性：
    Ubiquitously expressed; with highest levels in heart, liver and pancreas.
  • 數據庫鏈接：

    HGNC: 15672

    OMIM: 263210

    KEGG: hsa:79796

    STRING: 9606.ENSP00000435517

    UniGene: Hs.745155



主站蜘蛛池模板： 亚洲精品你懂的在线观看| 久久欧美与黑人双交男男| 成人aa免费视频在线播放| 欧美99久久无码一区人妻a片| 无遮挡18禁啪啪免费观看| 99久久精品免费看国产| 自拍偷在线精品自拍偷无码专区| 日韩精品一区二区三区vr| 亚洲腹肌男啪啪网站男同| av无码精品一区二区三区四区| 脱了美女内裤猛烈进入gif| 最新色国产精品精品视频| 欧美人与动牲交欧美精品| 国产无吗一区二区三区在线欢| 亚洲精品456在线播放| 国产在线精品无码二区| 亚洲高清国产拍精品26u| 天天爽夜夜爽人人爽曰| 国产无套乱子伦精彩是白视频| 亚洲a成人无m网站在线| 少妇激情作爱视频| 中文无码av一区二区三区| 狠狠色噜噜狠狠狠777米奇小说| 97超碰国产精品无码分类| 亚洲乱妇亚洲乱妇xinglu | 亚洲国产成人乱码| 人人爽人人模人人人爽人人爱| 日韩少妇激情一区二区| 日本欧美视频在线观看| 窝窝影院午夜看片| 成人电线在线播放无码| 国产交换配偶在线视频| 人妻丰满av无码久久不卡| 国产美足白丝榨精在线观看sm| 亚洲va中文字幕无码久久不卡| 无限看片在线版免费视频大全 | 乱子伦视频在线看| 中国熟妇牲交视频| 精品国产三级a在线观看网站| 女人高潮抽搐喷液30分钟视频| 欧美大肥婆大肥bbbbb|