在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

ALG1 Antibody

  • 中文名稱:
    ALG1兔多克隆抗體
  • 貨號:
    CSB-PA887118ESR2HU
  • 規格:
    ¥440
  • 圖片:
    • Immunohistochemistry of paraffin-embedded human breast cancer using CSB-PA887118ESR2HU at dilution of 1:100
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) ALG1 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    ALG1
  • 別名:
    4-mannosyltransferase antibody; Alg1 antibody; ALG1_HUMAN antibody; asparagine-linked glycosylation 1 homolog (yeast; beta-1,4-mannosyltransferase) antibody; asparagine-linked glycosylation 1; beta-1,4-mannosyltransferase homolog (S. cerevisiae) antibody; Asparagine-linked glycosylation protein 1 homolog antibody; Beta 1 4 mannosyltransferase antibody; Beta-1 antibody; CDG1K antibody; Chitobiosyldiphosphodolichol beta-mannosyltransferase antibody; GDP Man GlcNAc2 PP dolichol mannosyltransferase antibody; GDP-Man:GlcNAc2-PP-dolichol mannosyltransferase antibody; GDP-mannose-dolichol diphosphochitobiose mannosyltransferase antibody; Hmat-1 antibody; HMAT1 antibody; HMT 1 antibody; HMT1 antibody; Mannosyltransferase 1 antibody; Mannosyltransferase-1 antibody; MT 1 antibody; MT-1 antibody; MT1 antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Chitobiosyldiphosphodolichol beta-mannosyltransferase protein (215-464AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    Non-conjugated
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    Antigen Affinity Purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA, IHC
  • 推薦稀釋比:
    Application Recommended Dilution
    IHC 1:20-1:200
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Participates in the formation of the lipid-linked precursor oligosaccharide for N-glycosylation. Involved in assembling the dolichol-pyrophosphate-GlcNAc(2)-Man(5) intermediate on the cytoplasmic surface of the ER.
  • 基因功能參考文獻:
    1. evaluated the genetic association of WDR3 and ALG1 in schizophrenia. We examined 21 single nucleotide polymorphisms [SNPs; W1 (rs1812607)-W16 (rs6656360), A1 (rs8053916)-A10 (rs9673733)] from these genes using the Japanese case-control sample (1,808 schizophrenics and 2,170 matched controls). No significant genetic associations of these SNPs were identified. However, we detected a significant association of W4 (rs319471) PMID: 29309433
    2. Study presents molecular, clinical and biochemical findings in the largest collection of ALG1-CDG cases ever reported at a single time with 39 cases, bringing the total number to 57. This ranks it the third most common CDG type behind PMM2-CDG and ALG6-CDG. In addition, highly lethal genotype were identified and confirm the presence of a unique xeno-tetrasaccharide in ALG1-CDG patients. PMID: 26931382
    3. In title. PMID: 25649379
    4. Was detected in the patient's ALG1-coding sequence. PMID: 24157261
    5. Family study defining the phenotype of deficiency of beta-1,4 mannosyltransferase (MT-1) congenital disorder of glycosylation (CDG), due to ALG1 gene mutations. Four novel ALG1 mutations were identified. PMID: 22966035
    6. DNA sequencing of ALG1 revealed nine different mutations, seven of which have not been previously reported. Clinical presentations of deficiency are severe, with dysmorphias, CNS involvement and ocular disturbances PMID: 20679665

    顯示更多

    收起更多

  • 相關疾病:
    Congenital disorder of glycosylation 1K (CDG1K)
  • 亞細胞定位:
    Endoplasmic reticulum membrane; Single-pass type II membrane protein.
  • 蛋白家族:
    Glycosyltransferase group 1 family, Glycosyltransferase 33 subfamily
  • 數據庫鏈接:

    HGNC: 18294

    OMIM: 605907

    KEGG: hsa:56052

    STRING: 9606.ENSP00000262374

    UniGene: Hs.592086



主站蜘蛛池模板: 国产gv在线观看受被做哭| 风韵少妇性饥渴推油按摩视频| 国产特级毛片aaaaaa毛片| 2021年国产精品专区丝袜| 麻婆豆传媒一区二区三区| 2020国产在线拍揄自揄视频| 18禁在线永久免费观看| 亚洲乱亚洲乱少妇无码| 午夜伦4480yy私人影院久久| 2019国产品在线视频| 欧美颜射内射中出口爆在线| 精品人妻无码一区二区三区| 欧美最猛性xxxxx大叫| 亚洲bbw性色大片| 亚洲欧美另类久久久精品能播放的| 婷婷久久综合九色综合绿巨人| 国产成人一区二区无码不卡在线| 国产av午夜精品一区二区三区| 国产一区二区精品丝袜| 亚洲国产精品无码中文字满| 欧美极品video粗暴| 久久久一本精品久久精品六六| 巨大欧美黑人xxxxbbbb| 激情内射人妻1区2区3区| 无码h黄动漫在线播放网站 | 亚洲人成电影网站在线播放| 国产freexxxx性播放麻豆| 亚洲无人区码一码二码三码的含义| 国产av无码专区亚洲草草| 午夜色大片在线观看| 国产肥白大熟妇bbbb视频| 中文字幕日韩精品亚洲一区| 国产未成女一区二区| 色偷偷色噜噜狠狠网站久久 | 法国伦理少妇愉情| 波多野结衣网站| 久久99国产精品二区| 北条麻妃在线一区二区| 老司机午夜免费精品视频| 护士张开腿被奷日出白浆| 中日韩精品视频在线观看|