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Your Good Partner in Biology Research

ADCK4 Antibody

  • 中文名稱:
    ADCK4兔多克隆抗體
  • 貨號:
    CSB-PA990455
  • 規格:
    ¥2024
  • 圖片:
    • Western blot analysis of extracts from HepG2 cells, using ADCK4 antibody.
    • Immunofluorescence analysis of A549 cells, using ADCK4 antibody.
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) COQ8B Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    COQ8B
  • 別名:
    COQ8B; ADCK4; Atypical kinase COQ8B, mitochondrial; AarF domain-containing protein kinase 4; Coenzyme Q protein 8B
  • 宿主:
    Rabbit
  • 反應種屬:
    Human,Mouse,Rat
  • 免疫原:
    Synthesized peptide derived from internal of Human ADCK4.
  • 免疫原種屬:
    Homo sapiens (Human)
  • 克隆類型:
    Polyclonal
  • 純化方式:
    The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA,WB,IF
  • 推薦稀釋比:
    Application Recommended Dilution
    WB 1:500-1:3000
    IF 1:100-1:500
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Atypical kinase involved in the biosynthesis of coenzyme Q, also named ubiquinone, an essential lipid-soluble electron transporter for aerobic cellular respiration. Its substrate specificity is unclear: does not show any protein kinase activity. Probably acts as a small molecule kinase, possibly a lipid kinase that phosphorylates a prenyl lipid in the ubiquinone biosynthesis pathway. Required for podocyte migration.
  • 基因功能參考文獻:
    1. Mutations in ADCK4 resulted in reduced CoQ10 levels and reduced mitochondrial respiratory enzyme activity in cells isolated from individuals with steroid-resistant nephrotic syndrome & transformed lymphoblasts. PMID: 24270420
  • 相關疾病:
    Nephrotic syndrome 9 (NPHS9)
  • 亞細胞定位:
    Mitochondrion membrane; Single-pass membrane protein. Cytoplasm, cytosol. Cell membrane.
  • 蛋白家族:
    Protein kinase superfamily, ADCK protein kinase family
  • 組織特異性:
    Widely expressed, including renal podocytes.
  • 數據庫鏈接:

    HGNC: 19041

    OMIM: 615567

    KEGG: hsa:79934

    STRING: 9606.ENSP00000315118

    UniGene: Hs.130712



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