在线日韩日本国产亚洲丨少妇伦子伦情品无吗丨欧美性猛交xxxx免费看蜜桃丨精品人妻系列无码一区二区三区丨亚洲精品无码不卡在线播放

Your Good Partner in Biology Research

ACAD8 Antibody, HRP conjugated

  • 中文名稱:
    ACAD8兔多克隆抗體, HRP偶聯
  • 貨號:
    CSB-PA892457LB01HU
  • 規格:
    ¥880
  • 其他:

產品詳情

  • 產品名稱:
    Rabbit anti-Homo sapiens (Human) ACAD8 Polyclonal antibody
  • Uniprot No.:
  • 基因名:
    ACAD8
  • 別名:
    ACAD 8 antibody; ACAD-8 antibody; ACAD8 antibody; ACAD8_HUMAN antibody; Activator-recruited cofactor 42 kDa component antibody; Acyl CoA dehydrogenase family member 8 antibody; Acyl Coenzyme A dehydrogenase family member 8 antibody; Acyl-CoA dehydrogenase family member 8 antibody; ARC42 antibody; FLJ22590 antibody; IBD antibody; Isobutyryl-CoA dehydrogenase antibody; Isobutyryl-CoA dehydrogenase; mitochondrial antibody; mitochondrial antibody
  • 宿主:
    Rabbit
  • 反應種屬:
    Human
  • 免疫原:
    Recombinant Human Isobutyryl-CoA dehydrogenase, mitochondrial protein (201-415AA)
  • 免疫原種屬:
    Homo sapiens (Human)
  • 標記方式:
    HRP
  • 克隆類型:
    Polyclonal
  • 抗體亞型:
    IgG
  • 純化方式:
    >95%, Protein G purified
  • 濃度:
    It differs from different batches. Please contact us to confirm it.
  • 保存緩沖液:
    Preservative: 0.03% Proclin 300
    Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
  • 產品提供形式:
    Liquid
  • 應用范圍:
    ELISA
  • Protocols:
  • 儲存條件:
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 貨期:
    Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
  • 用途:
    For Research Use Only. Not for use in diagnostic or therapeutic procedures.

產品評價

靶點詳情

  • 功能:
    Isobutyryl-CoA dehydrogenase which catalyzes one of the steps of the valine catabolic pathway. To a lesser extent, is also able to catalyze the oxidation of (2S)-2-methylbutanoyl-CoA.
  • 基因功能參考文獻:
    1. we discovered a novel c.1156_1158delCAG mutation in ACAD8 in patients with isobutyryl-CoA dehydrogenase deficiency , and investigated the mutation spectrum of ACAD8. PMID: 24635911
    2. first enzymatic and molecular confirmation of a deficiency of this enzyme in a patient PMID: 12359132
  • 相關疾病:
    Isobutyryl-CoA dehydrogenase deficiency (IBDD)
  • 亞細胞定位:
    Mitochondrion.
  • 蛋白家族:
    Acyl-CoA dehydrogenase family
  • 組織特異性:
    Detected at comparable levels in all tissues examined (heart, lung, brain, skeletal muscle, pancreas and placenta). Weakly expressed in liver and kidney.
  • 數據庫鏈接:

    HGNC: 87

    OMIM: 604773

    KEGG: hsa:27034

    STRING: 9606.ENSP00000281182

    UniGene: Hs.14791



主站蜘蛛池模板: 乱人伦人妻中文字幕无码久久网 | 在线视+欧美+亚洲日本| 极品人妻少妇一区二区三区| 亚洲国产精品一区二区成人片| 久久天天躁狠狠躁夜夜avapp| 久久婷婷五月综合色精品| 无码写真精品永久福利在线| 精品亚洲国产成人av在线时间短的| 97性无码区免费| 久久亚洲精品无码观看不卡| 精品国产一区二区av麻豆| 国产东北肥熟老胖女| 一本一本久久a久久精品综合| 精品无人乱码一区二区三区的特点| 国产成人精品一区二区三区免费看 | 精品久久久久香蕉网 | 暖暖的在线观看日本社区| a∨在线视频播放| 亚洲综合色视频在线观看| 天天天天躁天天爱天天碰2018 | 曰本丰满熟妇xxxx性| 亚洲精品无码人妻无码| 亚洲成a∧人片在线播放调教| 99re8这里有精品热视频免费| 精品人妻无码专区中文字幕| 天堂а√中文最新版在线| 无码专区丰满人妻斩六十路| 亚洲男女一区二区三区| 欧美一区内射最近更新| 精品无码欧美黑人又粗又| 国精产品69永久中国有限| 国产乱人伦中文无无码视频试看| 永久黄网站色视频免费| 国产在线观看无码的免费网站 | 在线亚洲中文精品第1页| 国产精品福利一区二区| 99蜜桃臀久久久欧美精品网站| 2020最新无码福利视频| 美女裸免费观看网站| 黑人巨大精品欧美一区二区| 亚洲人成网站观看在线播放|